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An unusual variant of atrophic dermatofibrosarcoma protuberans

Dermatofibrosarcoma protuberans is an uncommon neoplasm that is most often seen in young adults. The most common clinical presentation is the protruding form; however, other subtypes are known, such as the atrophic. In 2012 there were only 33 reports of this variant in the literature. Many cases of...

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Detalles Bibliográficos
Autores principales: Aragão, Simone Silva da Costa, Leite, Everson José dos Santos, Cardoso, Alberto Eduardo Cox, Houly, Ricardo Luiz Simões
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Dermatologia 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5916409/
https://www.ncbi.nlm.nih.gov/pubmed/29723383
http://dx.doi.org/10.1590/abd1806-4841.20187049
Descripción
Sumario:Dermatofibrosarcoma protuberans is an uncommon neoplasm that is most often seen in young adults. The most common clinical presentation is the protruding form; however, other subtypes are known, such as the atrophic. In 2012 there were only 33 reports of this variant in the literature. Many cases of Dermatofibrosarcoma protuberans in children are only discovered in adulthood because they were not diagnosed early. Due the high morbidity, we raise the need for attention from the dermatologist to recognize uncommon neoplasms in the clinical practice. We report a case of a 15-year-old patient diagnosed with atrophic Dermatofibrosarcoma protuberans on the back.