Cargando…
An unusual variant of atrophic dermatofibrosarcoma protuberans
Dermatofibrosarcoma protuberans is an uncommon neoplasm that is most often seen in young adults. The most common clinical presentation is the protruding form; however, other subtypes are known, such as the atrophic. In 2012 there were only 33 reports of this variant in the literature. Many cases of...
Autores principales: | , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Sociedade Brasileira de Dermatologia
2018
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5916409/ https://www.ncbi.nlm.nih.gov/pubmed/29723383 http://dx.doi.org/10.1590/abd1806-4841.20187049 |
_version_ | 1783317008609181696 |
---|---|
author | Aragão, Simone Silva da Costa Leite, Everson José dos Santos Cardoso, Alberto Eduardo Cox Houly, Ricardo Luiz Simões |
author_facet | Aragão, Simone Silva da Costa Leite, Everson José dos Santos Cardoso, Alberto Eduardo Cox Houly, Ricardo Luiz Simões |
author_sort | Aragão, Simone Silva da Costa |
collection | PubMed |
description | Dermatofibrosarcoma protuberans is an uncommon neoplasm that is most often seen in young adults. The most common clinical presentation is the protruding form; however, other subtypes are known, such as the atrophic. In 2012 there were only 33 reports of this variant in the literature. Many cases of Dermatofibrosarcoma protuberans in children are only discovered in adulthood because they were not diagnosed early. Due the high morbidity, we raise the need for attention from the dermatologist to recognize uncommon neoplasms in the clinical practice. We report a case of a 15-year-old patient diagnosed with atrophic Dermatofibrosarcoma protuberans on the back. |
format | Online Article Text |
id | pubmed-5916409 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | Sociedade Brasileira de Dermatologia |
record_format | MEDLINE/PubMed |
spelling | pubmed-59164092018-04-30 An unusual variant of atrophic dermatofibrosarcoma protuberans Aragão, Simone Silva da Costa Leite, Everson José dos Santos Cardoso, Alberto Eduardo Cox Houly, Ricardo Luiz Simões An Bras Dermatol Case Report Dermatofibrosarcoma protuberans is an uncommon neoplasm that is most often seen in young adults. The most common clinical presentation is the protruding form; however, other subtypes are known, such as the atrophic. In 2012 there were only 33 reports of this variant in the literature. Many cases of Dermatofibrosarcoma protuberans in children are only discovered in adulthood because they were not diagnosed early. Due the high morbidity, we raise the need for attention from the dermatologist to recognize uncommon neoplasms in the clinical practice. We report a case of a 15-year-old patient diagnosed with atrophic Dermatofibrosarcoma protuberans on the back. Sociedade Brasileira de Dermatologia 2018 /pmc/articles/PMC5916409/ /pubmed/29723383 http://dx.doi.org/10.1590/abd1806-4841.20187049 Text en http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial No Derivative License, which permits unrestricted non-commercial use, distribution, and reproduction in any medium provided the original work is properly cited and the work is not changed in any way. |
spellingShingle | Case Report Aragão, Simone Silva da Costa Leite, Everson José dos Santos Cardoso, Alberto Eduardo Cox Houly, Ricardo Luiz Simões An unusual variant of atrophic dermatofibrosarcoma protuberans |
title | An unusual variant of atrophic dermatofibrosarcoma protuberans |
title_full | An unusual variant of atrophic dermatofibrosarcoma protuberans |
title_fullStr | An unusual variant of atrophic dermatofibrosarcoma protuberans |
title_full_unstemmed | An unusual variant of atrophic dermatofibrosarcoma protuberans |
title_short | An unusual variant of atrophic dermatofibrosarcoma protuberans |
title_sort | unusual variant of atrophic dermatofibrosarcoma protuberans |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5916409/ https://www.ncbi.nlm.nih.gov/pubmed/29723383 http://dx.doi.org/10.1590/abd1806-4841.20187049 |
work_keys_str_mv | AT aragaosimonesilvadacosta anunusualvariantofatrophicdermatofibrosarcomaprotuberans AT leiteeversonjosedossantos anunusualvariantofatrophicdermatofibrosarcomaprotuberans AT cardosoalbertoeduardocox anunusualvariantofatrophicdermatofibrosarcomaprotuberans AT houlyricardoluizsimoes anunusualvariantofatrophicdermatofibrosarcomaprotuberans AT aragaosimonesilvadacosta unusualvariantofatrophicdermatofibrosarcomaprotuberans AT leiteeversonjosedossantos unusualvariantofatrophicdermatofibrosarcomaprotuberans AT cardosoalbertoeduardocox unusualvariantofatrophicdermatofibrosarcomaprotuberans AT houlyricardoluizsimoes unusualvariantofatrophicdermatofibrosarcomaprotuberans |