Cargando…

An unusual variant of atrophic dermatofibrosarcoma protuberans

Dermatofibrosarcoma protuberans is an uncommon neoplasm that is most often seen in young adults. The most common clinical presentation is the protruding form; however, other subtypes are known, such as the atrophic. In 2012 there were only 33 reports of this variant in the literature. Many cases of...

Descripción completa

Detalles Bibliográficos
Autores principales: Aragão, Simone Silva da Costa, Leite, Everson José dos Santos, Cardoso, Alberto Eduardo Cox, Houly, Ricardo Luiz Simões
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Dermatologia 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5916409/
https://www.ncbi.nlm.nih.gov/pubmed/29723383
http://dx.doi.org/10.1590/abd1806-4841.20187049
_version_ 1783317008609181696
author Aragão, Simone Silva da Costa
Leite, Everson José dos Santos
Cardoso, Alberto Eduardo Cox
Houly, Ricardo Luiz Simões
author_facet Aragão, Simone Silva da Costa
Leite, Everson José dos Santos
Cardoso, Alberto Eduardo Cox
Houly, Ricardo Luiz Simões
author_sort Aragão, Simone Silva da Costa
collection PubMed
description Dermatofibrosarcoma protuberans is an uncommon neoplasm that is most often seen in young adults. The most common clinical presentation is the protruding form; however, other subtypes are known, such as the atrophic. In 2012 there were only 33 reports of this variant in the literature. Many cases of Dermatofibrosarcoma protuberans in children are only discovered in adulthood because they were not diagnosed early. Due the high morbidity, we raise the need for attention from the dermatologist to recognize uncommon neoplasms in the clinical practice. We report a case of a 15-year-old patient diagnosed with atrophic Dermatofibrosarcoma protuberans on the back.
format Online
Article
Text
id pubmed-5916409
institution National Center for Biotechnology Information
language English
publishDate 2018
publisher Sociedade Brasileira de Dermatologia
record_format MEDLINE/PubMed
spelling pubmed-59164092018-04-30 An unusual variant of atrophic dermatofibrosarcoma protuberans Aragão, Simone Silva da Costa Leite, Everson José dos Santos Cardoso, Alberto Eduardo Cox Houly, Ricardo Luiz Simões An Bras Dermatol Case Report Dermatofibrosarcoma protuberans is an uncommon neoplasm that is most often seen in young adults. The most common clinical presentation is the protruding form; however, other subtypes are known, such as the atrophic. In 2012 there were only 33 reports of this variant in the literature. Many cases of Dermatofibrosarcoma protuberans in children are only discovered in adulthood because they were not diagnosed early. Due the high morbidity, we raise the need for attention from the dermatologist to recognize uncommon neoplasms in the clinical practice. We report a case of a 15-year-old patient diagnosed with atrophic Dermatofibrosarcoma protuberans on the back. Sociedade Brasileira de Dermatologia 2018 /pmc/articles/PMC5916409/ /pubmed/29723383 http://dx.doi.org/10.1590/abd1806-4841.20187049 Text en http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial No Derivative License, which permits unrestricted non-commercial use, distribution, and reproduction in any medium provided the original work is properly cited and the work is not changed in any way.
spellingShingle Case Report
Aragão, Simone Silva da Costa
Leite, Everson José dos Santos
Cardoso, Alberto Eduardo Cox
Houly, Ricardo Luiz Simões
An unusual variant of atrophic dermatofibrosarcoma protuberans
title An unusual variant of atrophic dermatofibrosarcoma protuberans
title_full An unusual variant of atrophic dermatofibrosarcoma protuberans
title_fullStr An unusual variant of atrophic dermatofibrosarcoma protuberans
title_full_unstemmed An unusual variant of atrophic dermatofibrosarcoma protuberans
title_short An unusual variant of atrophic dermatofibrosarcoma protuberans
title_sort unusual variant of atrophic dermatofibrosarcoma protuberans
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5916409/
https://www.ncbi.nlm.nih.gov/pubmed/29723383
http://dx.doi.org/10.1590/abd1806-4841.20187049
work_keys_str_mv AT aragaosimonesilvadacosta anunusualvariantofatrophicdermatofibrosarcomaprotuberans
AT leiteeversonjosedossantos anunusualvariantofatrophicdermatofibrosarcomaprotuberans
AT cardosoalbertoeduardocox anunusualvariantofatrophicdermatofibrosarcomaprotuberans
AT houlyricardoluizsimoes anunusualvariantofatrophicdermatofibrosarcomaprotuberans
AT aragaosimonesilvadacosta unusualvariantofatrophicdermatofibrosarcomaprotuberans
AT leiteeversonjosedossantos unusualvariantofatrophicdermatofibrosarcomaprotuberans
AT cardosoalbertoeduardocox unusualvariantofatrophicdermatofibrosarcomaprotuberans
AT houlyricardoluizsimoes unusualvariantofatrophicdermatofibrosarcomaprotuberans