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Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS

Unilateral pulmonary artery agenesis (UPAA) is a rare malformation that can present as an isolated anomaly or may be associated with certain congenital cardiac anomalies, such as tetralogy of Fallot, atrial septal defect, coarctation of aorta, right aortic arch, truncus arteriosus and pulmonary atre...

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Autores principales: Saladi, Lakshmi, Roy, Swati, Diaz-Fuentes, Gilda
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5925952/
https://www.ncbi.nlm.nih.gov/pubmed/29719804
http://dx.doi.org/10.1016/j.rmcr.2018.02.004
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author Saladi, Lakshmi
Roy, Swati
Diaz-Fuentes, Gilda
author_facet Saladi, Lakshmi
Roy, Swati
Diaz-Fuentes, Gilda
author_sort Saladi, Lakshmi
collection PubMed
description Unilateral pulmonary artery agenesis (UPAA) is a rare malformation that can present as an isolated anomaly or may be associated with certain congenital cardiac anomalies, such as tetralogy of Fallot, atrial septal defect, coarctation of aorta, right aortic arch, truncus arteriosus and pulmonary atresia. Clinical presentation is non-specific which makes the diagnosis elusive; chronic dyspnea, hemoptysis or recurrent infections are the most common manifestations. Patients may remain asymptomatic until adulthood. There is no definitive treatment for patients with UPAA. Acute respiratory distress syndrome (ARDS) is usually a bilateral disease, unilateral ARDS has been described after lung resection or trauma. We present a case of a 39 year-old woman who developed unilateral ARDS and was later diagnosed with isolated UPAA.
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spelling pubmed-59259522018-05-01 Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS Saladi, Lakshmi Roy, Swati Diaz-Fuentes, Gilda Respir Med Case Rep Case Report Unilateral pulmonary artery agenesis (UPAA) is a rare malformation that can present as an isolated anomaly or may be associated with certain congenital cardiac anomalies, such as tetralogy of Fallot, atrial septal defect, coarctation of aorta, right aortic arch, truncus arteriosus and pulmonary atresia. Clinical presentation is non-specific which makes the diagnosis elusive; chronic dyspnea, hemoptysis or recurrent infections are the most common manifestations. Patients may remain asymptomatic until adulthood. There is no definitive treatment for patients with UPAA. Acute respiratory distress syndrome (ARDS) is usually a bilateral disease, unilateral ARDS has been described after lung resection or trauma. We present a case of a 39 year-old woman who developed unilateral ARDS and was later diagnosed with isolated UPAA. Elsevier 2018-02-21 /pmc/articles/PMC5925952/ /pubmed/29719804 http://dx.doi.org/10.1016/j.rmcr.2018.02.004 Text en © 2018 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Saladi, Lakshmi
Roy, Swati
Diaz-Fuentes, Gilda
Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS
title Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS
title_full Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS
title_fullStr Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS
title_full_unstemmed Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS
title_short Unilateral pulmonary artery agenesis: An unusual cause of unilateral ARDS
title_sort unilateral pulmonary artery agenesis: an unusual cause of unilateral ards
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5925952/
https://www.ncbi.nlm.nih.gov/pubmed/29719804
http://dx.doi.org/10.1016/j.rmcr.2018.02.004
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