Large granular lymphocytic leukemia complicating autoimmune polyglandular syndrome type 1 in siblings

Autoimmune polyglandular syndrome type 1 (APS1) is a rare autosomal recessive disorder, and large granular lymphocytic leukemia (LGLL) may, even more rarely, complicate APS1. LGLL may be subtle in presentation, but it is imperative to recognize LGLL in APS1 promptly, as outcome may otherwise be fata...

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Detalles Bibliográficos
Autores principales: Harrison, Jonathan S., Parmar, Harsh, Wang, Xiangbing D.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2018
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5930195/
https://www.ncbi.nlm.nih.gov/pubmed/29744070
http://dx.doi.org/10.1002/ccr3.1454
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author Harrison, Jonathan S.
Parmar, Harsh
Wang, Xiangbing D.
author_facet Harrison, Jonathan S.
Parmar, Harsh
Wang, Xiangbing D.
author_sort Harrison, Jonathan S.
collection PubMed
description Autoimmune polyglandular syndrome type 1 (APS1) is a rare autosomal recessive disorder, and large granular lymphocytic leukemia (LGLL) may, even more rarely, complicate APS1. LGLL may be subtle in presentation, but it is imperative to recognize LGLL in APS1 promptly, as outcome may otherwise be fatal, as described herein.
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spelling pubmed-59301952018-05-09 Large granular lymphocytic leukemia complicating autoimmune polyglandular syndrome type 1 in siblings Harrison, Jonathan S. Parmar, Harsh Wang, Xiangbing D. Clin Case Rep Case Reports Autoimmune polyglandular syndrome type 1 (APS1) is a rare autosomal recessive disorder, and large granular lymphocytic leukemia (LGLL) may, even more rarely, complicate APS1. LGLL may be subtle in presentation, but it is imperative to recognize LGLL in APS1 promptly, as outcome may otherwise be fatal, as described herein. John Wiley and Sons Inc. 2018-03-11 /pmc/articles/PMC5930195/ /pubmed/29744070 http://dx.doi.org/10.1002/ccr3.1454 Text en © 2018 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. This is an open access article under the terms of the http://creativecommons.org/licenses/by/4.0/ License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Reports
Harrison, Jonathan S.
Parmar, Harsh
Wang, Xiangbing D.
Large granular lymphocytic leukemia complicating autoimmune polyglandular syndrome type 1 in siblings
title Large granular lymphocytic leukemia complicating autoimmune polyglandular syndrome type 1 in siblings
title_full Large granular lymphocytic leukemia complicating autoimmune polyglandular syndrome type 1 in siblings
title_fullStr Large granular lymphocytic leukemia complicating autoimmune polyglandular syndrome type 1 in siblings
title_full_unstemmed Large granular lymphocytic leukemia complicating autoimmune polyglandular syndrome type 1 in siblings
title_short Large granular lymphocytic leukemia complicating autoimmune polyglandular syndrome type 1 in siblings
title_sort large granular lymphocytic leukemia complicating autoimmune polyglandular syndrome type 1 in siblings
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5930195/
https://www.ncbi.nlm.nih.gov/pubmed/29744070
http://dx.doi.org/10.1002/ccr3.1454
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AT wangxiangbingd largegranularlymphocyticleukemiacomplicatingautoimmunepolyglandularsyndrometype1insiblings

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