Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome

Patients with congenital agenesis of the portal vein may develop hepatocellular tumors due to enhanced arterial blood flow. These tumors may be benign (FNH, adenomas) or malignant (hepatoblastoma, HCC). Liver resection can be proposed, and preoperative arterial embolization may decrease blood loss d...

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Detalles Bibliográficos
Autores principales: Christou, Niki, Dib, Nabil, Chuffart, Etienne, Taibi, Abdelkader, Durand‐Fontanier, Sylvaine, Valleix, Denis, Mathonnet, Muriel
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2018
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5930207/
https://www.ncbi.nlm.nih.gov/pubmed/29744090
http://dx.doi.org/10.1002/ccr3.1384
Descripción
Sumario:Patients with congenital agenesis of the portal vein may develop hepatocellular tumors due to enhanced arterial blood flow. These tumors may be benign (FNH, adenomas) or malignant (hepatoblastoma, HCC). Liver resection can be proposed, and preoperative arterial embolization may decrease blood loss during surgery. Liver transplantation with PV reconstruction is also an option.

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