Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome

Patients with congenital agenesis of the portal vein may develop hepatocellular tumors due to enhanced arterial blood flow. These tumors may be benign (FNH, adenomas) or malignant (hepatoblastoma, HCC). Liver resection can be proposed, and preoperative arterial embolization may decrease blood loss d...

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Autores principales: Christou, Niki, Dib, Nabil, Chuffart, Etienne, Taibi, Abdelkader, Durand‐Fontanier, Sylvaine, Valleix, Denis, Mathonnet, Muriel
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2018
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5930207/
https://www.ncbi.nlm.nih.gov/pubmed/29744090
http://dx.doi.org/10.1002/ccr3.1384
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author Christou, Niki
Dib, Nabil
Chuffart, Etienne
Taibi, Abdelkader
Durand‐Fontanier, Sylvaine
Valleix, Denis
Mathonnet, Muriel
author_facet Christou, Niki
Dib, Nabil
Chuffart, Etienne
Taibi, Abdelkader
Durand‐Fontanier, Sylvaine
Valleix, Denis
Mathonnet, Muriel
author_sort Christou, Niki
collection PubMed
description Patients with congenital agenesis of the portal vein may develop hepatocellular tumors due to enhanced arterial blood flow. These tumors may be benign (FNH, adenomas) or malignant (hepatoblastoma, HCC). Liver resection can be proposed, and preoperative arterial embolization may decrease blood loss during surgery. Liver transplantation with PV reconstruction is also an option.
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spelling pubmed-59302072018-05-09 Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome Christou, Niki Dib, Nabil Chuffart, Etienne Taibi, Abdelkader Durand‐Fontanier, Sylvaine Valleix, Denis Mathonnet, Muriel Clin Case Rep Case Reports Patients with congenital agenesis of the portal vein may develop hepatocellular tumors due to enhanced arterial blood flow. These tumors may be benign (FNH, adenomas) or malignant (hepatoblastoma, HCC). Liver resection can be proposed, and preoperative arterial embolization may decrease blood loss during surgery. Liver transplantation with PV reconstruction is also an option. John Wiley and Sons Inc. 2018-03-30 /pmc/articles/PMC5930207/ /pubmed/29744090 http://dx.doi.org/10.1002/ccr3.1384 Text en © 2018 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. This is an open access article under the terms of the http://creativecommons.org/licenses/by/4.0/ License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Reports
Christou, Niki
Dib, Nabil
Chuffart, Etienne
Taibi, Abdelkader
Durand‐Fontanier, Sylvaine
Valleix, Denis
Mathonnet, Muriel
Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome
title Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome
title_full Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome
title_fullStr Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome
title_full_unstemmed Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome
title_short Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome
title_sort stepwise management of hepatocellular carcinoma associated with abernethy syndrome
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5930207/
https://www.ncbi.nlm.nih.gov/pubmed/29744090
http://dx.doi.org/10.1002/ccr3.1384
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