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A total pleural covering of absorbable cellulose mesh prevents pneumothorax recurrence in patients with Birt-Hogg-Dubé syndrome
BACKGROUND: Birt-Hogg-Dubé syndrome (BHDS) is a recently recognized inherited multiple cystic lung disease causing recurrent pneumothoraces. Similarly to the lesions in patients with lymphangioleiomyomatosis (LAM), the pulmonary cysts are innumerable and widely dispersed and cannot all be removed. W...
Autores principales: | Mizobuchi, Teruaki, Kurihara, Masatoshi, Ebana, Hiroki, Yamanaka, Sumitaka, Kataoka, Hideyuki, Okamoto, Shouichi, Kobayashi, Etsuko, Kumasaka, Toshio, Seyama, Kuniaki |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5952889/ https://www.ncbi.nlm.nih.gov/pubmed/29764481 http://dx.doi.org/10.1186/s13023-018-0790-x |
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