Risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders

Totally implantable vascular access devices (TIVADs) are commonly used in conjunction with enzyme replacement therapy (ERT) for lysosomal storage disorders (LSDs). This case series describes potential complications associated with long-term TIVAD use, such as compromise of skin integrity, infection,...

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Detalles Bibliográficos
Autores principales: Hendriksz, Christian J., Harmatz, Paul, Giugliani, Roberto, Roberts, Jane, Arul, G. Suren
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2018
Materias:
Research Paper
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5966583/
https://www.ncbi.nlm.nih.gov/pubmed/29845015
http://dx.doi.org/10.1016/j.ymgmr.2018.02.007
Descripción
Sumario:Totally implantable vascular access devices (TIVADs) are commonly used in conjunction with enzyme replacement therapy (ERT) for lysosomal storage disorders (LSDs). This case series describes potential complications associated with long-term TIVAD use, such as compromise of skin integrity, infection, or port failures. Best practices and skilled specialists are essential for minimizing complications from long-term TIVAD use for ERT.

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