Risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders

Totally implantable vascular access devices (TIVADs) are commonly used in conjunction with enzyme replacement therapy (ERT) for lysosomal storage disorders (LSDs). This case series describes potential complications associated with long-term TIVAD use, such as compromise of skin integrity, infection,...

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Detalles Bibliográficos
Autores principales: Hendriksz, Christian J., Harmatz, Paul, Giugliani, Roberto, Roberts, Jane, Arul, G. Suren
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2018
Materias:
Research Paper
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5966583/
https://www.ncbi.nlm.nih.gov/pubmed/29845015
http://dx.doi.org/10.1016/j.ymgmr.2018.02.007
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author Hendriksz, Christian J.
Harmatz, Paul
Giugliani, Roberto
Roberts, Jane
Arul, G. Suren
author_facet Hendriksz, Christian J.
Harmatz, Paul
Giugliani, Roberto
Roberts, Jane
Arul, G. Suren
author_sort Hendriksz, Christian J.
collection PubMed
description Totally implantable vascular access devices (TIVADs) are commonly used in conjunction with enzyme replacement therapy (ERT) for lysosomal storage disorders (LSDs). This case series describes potential complications associated with long-term TIVAD use, such as compromise of skin integrity, infection, or port failures. Best practices and skilled specialists are essential for minimizing complications from long-term TIVAD use for ERT.
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spelling pubmed-59665832018-05-29 Risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders Hendriksz, Christian J. Harmatz, Paul Giugliani, Roberto Roberts, Jane Arul, G. Suren Mol Genet Metab Rep Research Paper Totally implantable vascular access devices (TIVADs) are commonly used in conjunction with enzyme replacement therapy (ERT) for lysosomal storage disorders (LSDs). This case series describes potential complications associated with long-term TIVAD use, such as compromise of skin integrity, infection, or port failures. Best practices and skilled specialists are essential for minimizing complications from long-term TIVAD use for ERT. Elsevier 2018-03-07 /pmc/articles/PMC5966583/ /pubmed/29845015 http://dx.doi.org/10.1016/j.ymgmr.2018.02.007 Text en © 2018 The Authors http://creativecommons.org/licenses/by/4.0/ This is an open access article under the CC BY license (http://creativecommons.org/licenses/by/4.0/).
spellingShingle Research Paper
Hendriksz, Christian J.
Harmatz, Paul
Giugliani, Roberto
Roberts, Jane
Arul, G. Suren
Risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders
title Risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders
title_full Risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders
title_fullStr Risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders
title_full_unstemmed Risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders
title_short Risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders
title_sort risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders
topic Research Paper
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5966583/
https://www.ncbi.nlm.nih.gov/pubmed/29845015
http://dx.doi.org/10.1016/j.ymgmr.2018.02.007
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