Cargando…
Modulating membrane fluidity corrects Batten disease phenotypes in vitro and in vivo
The neuronal ceroid lipofuscinoses are a class of inherited neurodegenerative diseases characterized by the accumulation of autofluorescent storage material. The most common neuronal ceroid lipofuscinosis has juvenile onset with rapid onset blindness and progressive degeneration of cognitive process...
Autores principales: | Schultz, Mark L., Tecedor, Luis, Lysenko, Elena, Ramachandran, Shyam, Stein, Colleen S., Davidson, Beverly L. |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
2018
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5969532/ https://www.ncbi.nlm.nih.gov/pubmed/29660499 http://dx.doi.org/10.1016/j.nbd.2018.04.010 |
Ejemplares similares
-
CLN3 Deficient Cells Display Defects in the ARF1-Cdc42 Pathway and Actin-Dependent Events
por: Schultz, Mark L., et al.
Publicado: (2014) -
Cellular models of Batten disease
por: Minnis, Christopher J., et al.
Publicado: (2020) -
Rho Signaling Participates in Membrane Fluidity Homeostasis
por: Lockshon, Daniel, et al.
Publicado: (2012) -
Membrane homeostasis beyond fluidity: control of membrane compressibility
por: Renne, Mike F., et al.
Publicado: (2023) -
Autophagy in the Neuronal Ceroid Lipofuscinoses (Batten Disease)
por: Kim, William D., et al.
Publicado: (2022)