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Invertebrate models of lamin diseases
Lamins are evolutionarily conserved nuclear intermediate filament proteins. They provide structural support for the nucleus and help regulate many other nuclear activities. Mutations in human lamin genes, and especially in the LMNA gene, cause numerous diseases, termed laminopathies, including muscl...
Autores principales: | Rzepecki, Ryszard, Gruenbaum, Yosef |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Taylor & Francis
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5973256/ https://www.ncbi.nlm.nih.gov/pubmed/29557730 http://dx.doi.org/10.1080/19491034.2018.1454166 |
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