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Lipodystrophic laminopathies: Diagnostic clues
The nuclear lamina is a complex reticular structure that covers the inner face of the nucleus membrane in metazoan cells. It is mainly formed by intermediate filaments called lamins, and exerts essential functions to maintain the cellular viability. Lamin A/C provides mechanical steadiness to the nu...
Autores principales: | Guillín-Amarelle, Cristina, Fernández-Pombo, Antía, Sánchez-Iglesias, Sofía, Araújo-Vilar, David |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Taylor & Francis
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5973260/ https://www.ncbi.nlm.nih.gov/pubmed/29557732 http://dx.doi.org/10.1080/19491034.2018.1454167 |
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