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Extensive Cranial Nerves Involvement in Neurofibromatosis: A Rare Presentation
Neurofibromatosis type 2 is a rare neurocutaneous syndrome characterized by the development of multiple nervous system tumors. This disorder is also called multiple inherited schwannomas, meningiomas, and ependymomas syndrome. In this report, we discuss the clinical and magnetic resonance imaging fi...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5982496/ https://www.ncbi.nlm.nih.gov/pubmed/29899775 http://dx.doi.org/10.4103/JPN.JPN_32_18 |
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author | Gupta, Ashutosh Gupta, Charu Sachan, Monika Singh, Sandeep |
author_facet | Gupta, Ashutosh Gupta, Charu Sachan, Monika Singh, Sandeep |
author_sort | Gupta, Ashutosh |
collection | PubMed |
description | Neurofibromatosis type 2 is a rare neurocutaneous syndrome characterized by the development of multiple nervous system tumors. This disorder is also called multiple inherited schwannomas, meningiomas, and ependymomas syndrome. In this report, we discuss the clinical and magnetic resonance imaging findings in a 17-year-old patient with neurofibromatosis type 2, who had extensive cranial nerves involvement (3rd–12th cranial nerves) along with spinal involvement. It is very rare to find tumors affect nearly all cranial nerves (namely 3rd–12th nerves), and their association with meningiomas and intramedullary spinal cord tumors in the same patient. |
format | Online Article Text |
id | pubmed-5982496 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-59824962018-06-13 Extensive Cranial Nerves Involvement in Neurofibromatosis: A Rare Presentation Gupta, Ashutosh Gupta, Charu Sachan, Monika Singh, Sandeep J Pediatr Neurosci Case Report Neurofibromatosis type 2 is a rare neurocutaneous syndrome characterized by the development of multiple nervous system tumors. This disorder is also called multiple inherited schwannomas, meningiomas, and ependymomas syndrome. In this report, we discuss the clinical and magnetic resonance imaging findings in a 17-year-old patient with neurofibromatosis type 2, who had extensive cranial nerves involvement (3rd–12th cranial nerves) along with spinal involvement. It is very rare to find tumors affect nearly all cranial nerves (namely 3rd–12th nerves), and their association with meningiomas and intramedullary spinal cord tumors in the same patient. Medknow Publications & Media Pvt Ltd 2018 /pmc/articles/PMC5982496/ /pubmed/29899775 http://dx.doi.org/10.4103/JPN.JPN_32_18 Text en Copyright: © 2018 Journal of Pediatric Neurosciences http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Gupta, Ashutosh Gupta, Charu Sachan, Monika Singh, Sandeep Extensive Cranial Nerves Involvement in Neurofibromatosis: A Rare Presentation |
title | Extensive Cranial Nerves Involvement in Neurofibromatosis: A Rare Presentation |
title_full | Extensive Cranial Nerves Involvement in Neurofibromatosis: A Rare Presentation |
title_fullStr | Extensive Cranial Nerves Involvement in Neurofibromatosis: A Rare Presentation |
title_full_unstemmed | Extensive Cranial Nerves Involvement in Neurofibromatosis: A Rare Presentation |
title_short | Extensive Cranial Nerves Involvement in Neurofibromatosis: A Rare Presentation |
title_sort | extensive cranial nerves involvement in neurofibromatosis: a rare presentation |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5982496/ https://www.ncbi.nlm.nih.gov/pubmed/29899775 http://dx.doi.org/10.4103/JPN.JPN_32_18 |
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