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Abnormalities in Skeletal Muscle Myogenesis, Growth, and Regeneration in Myotonic Dystrophy

Myotonic dystrophy type 1 (DM1) and 2 (DM2) are autosomal dominant degenerative neuromuscular disorders characterized by progressive skeletal muscle weakness, atrophy, and myotonia with progeroid features. Although both DM1 and DM2 are characterized by skeletal muscle dysfunction and also share othe...

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Detalles Bibliográficos
Autores principales:	André, Laurène M., Ausems, C. Rosanne M., Wansink, Derick G., Wieringa, Bé
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2018
Materias:	Neuroscience
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5985300/ https://www.ncbi.nlm.nih.gov/pubmed/29892259 http://dx.doi.org/10.3389/fneur.2018.00368

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