A young woman with steroid‐responsive, IgG4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites

Lymphangiomas are benign tumors of the lymphatic vessels, which can be inflammatory and occasionally steroid‐responsive. IgG4‐related disease (IgG4‐RD) is a recently defined fibro‐inflammatory condition. We describe a novel association between reactive IgG4+ plasma cells and cystic lymphangioma in a...

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Detalles Bibliográficos
Autores principales: Al Zaki, Alaa A., Mann, Shawna L., Carruthers, Mollie N., Slack, Graham W., Chen, Luke Y. C.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2018
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5985987/
https://www.ncbi.nlm.nih.gov/pubmed/29881573
http://dx.doi.org/10.1002/ccr3.1536
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author Al Zaki, Alaa A.
Mann, Shawna L.
Carruthers, Mollie N.
Slack, Graham W.
Chen, Luke Y. C.
author_facet Al Zaki, Alaa A.
Mann, Shawna L.
Carruthers, Mollie N.
Slack, Graham W.
Chen, Luke Y. C.
author_sort Al Zaki, Alaa A.
collection PubMed
description Lymphangiomas are benign tumors of the lymphatic vessels, which can be inflammatory and occasionally steroid‐responsive. IgG4‐related disease (IgG4‐RD) is a recently defined fibro‐inflammatory condition. We describe a novel association between reactive IgG4+ plasma cells and cystic lymphangioma in a young woman who had a dramatic clinical response to steroids.
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spelling pubmed-59859872018-06-07 A young woman with steroid‐responsive, IgG4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites Al Zaki, Alaa A. Mann, Shawna L. Carruthers, Mollie N. Slack, Graham W. Chen, Luke Y. C. Clin Case Rep Case Reports Lymphangiomas are benign tumors of the lymphatic vessels, which can be inflammatory and occasionally steroid‐responsive. IgG4‐related disease (IgG4‐RD) is a recently defined fibro‐inflammatory condition. We describe a novel association between reactive IgG4+ plasma cells and cystic lymphangioma in a young woman who had a dramatic clinical response to steroids. John Wiley and Sons Inc. 2018-04-17 /pmc/articles/PMC5985987/ /pubmed/29881573 http://dx.doi.org/10.1002/ccr3.1536 Text en © 2018 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. This is an open access article under the terms of the http://creativecommons.org/licenses/by/4.0/ License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Reports
Al Zaki, Alaa A.
Mann, Shawna L.
Carruthers, Mollie N.
Slack, Graham W.
Chen, Luke Y. C.
A young woman with steroid‐responsive, IgG4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites
title A young woman with steroid‐responsive, IgG4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites
title_full A young woman with steroid‐responsive, IgG4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites
title_fullStr A young woman with steroid‐responsive, IgG4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites
title_full_unstemmed A young woman with steroid‐responsive, IgG4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites
title_short A young woman with steroid‐responsive, IgG4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites
title_sort young woman with steroid‐responsive, igg4‐positive plasma cell‐enriched cystic lymphangioma and chylous ascites
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5985987/
https://www.ncbi.nlm.nih.gov/pubmed/29881573
http://dx.doi.org/10.1002/ccr3.1536
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