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Lymphocytic interstitial pneumonia in a patient with mixed connective tissue disease – A case report

Lymphocytic interstitial pneumonia (LIP) is an uncommon interstitial lung disease that is characterized by an interstitial infiltrate of lymphoplasmacytic cells. While idiopathic LIP appears to be extremely rare, most reported cases of LIP have been associated with coexisting immune derangements, pa...

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Autores principales: Kuo, Chin-Wei, Chang, Kung-Chao, Chang, Han-Yu, Huang, Tang-Hsiu
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5991914/
https://www.ncbi.nlm.nih.gov/pubmed/29892541
http://dx.doi.org/10.1016/j.rmcr.2018.06.003
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author Kuo, Chin-Wei
Chang, Kung-Chao
Chang, Han-Yu
Huang, Tang-Hsiu
author_facet Kuo, Chin-Wei
Chang, Kung-Chao
Chang, Han-Yu
Huang, Tang-Hsiu
author_sort Kuo, Chin-Wei
collection PubMed
description Lymphocytic interstitial pneumonia (LIP) is an uncommon interstitial lung disease that is characterized by an interstitial infiltrate of lymphoplasmacytic cells. While idiopathic LIP appears to be extremely rare, most reported cases of LIP have been associated with coexisting immune derangements, particularly autoimmune diseases such as Sjögren's syndrome. In this report, we describe the presentation of LIP in a patient with underlying mixed connective tissue disease.
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spelling pubmed-59919142018-06-11 Lymphocytic interstitial pneumonia in a patient with mixed connective tissue disease – A case report Kuo, Chin-Wei Chang, Kung-Chao Chang, Han-Yu Huang, Tang-Hsiu Respir Med Case Rep Case Report Lymphocytic interstitial pneumonia (LIP) is an uncommon interstitial lung disease that is characterized by an interstitial infiltrate of lymphoplasmacytic cells. While idiopathic LIP appears to be extremely rare, most reported cases of LIP have been associated with coexisting immune derangements, particularly autoimmune diseases such as Sjögren's syndrome. In this report, we describe the presentation of LIP in a patient with underlying mixed connective tissue disease. Elsevier 2018-06-05 /pmc/articles/PMC5991914/ /pubmed/29892541 http://dx.doi.org/10.1016/j.rmcr.2018.06.003 Text en © 2018 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Kuo, Chin-Wei
Chang, Kung-Chao
Chang, Han-Yu
Huang, Tang-Hsiu
Lymphocytic interstitial pneumonia in a patient with mixed connective tissue disease – A case report
title Lymphocytic interstitial pneumonia in a patient with mixed connective tissue disease – A case report
title_full Lymphocytic interstitial pneumonia in a patient with mixed connective tissue disease – A case report
title_fullStr Lymphocytic interstitial pneumonia in a patient with mixed connective tissue disease – A case report
title_full_unstemmed Lymphocytic interstitial pneumonia in a patient with mixed connective tissue disease – A case report
title_short Lymphocytic interstitial pneumonia in a patient with mixed connective tissue disease – A case report
title_sort lymphocytic interstitial pneumonia in a patient with mixed connective tissue disease – a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5991914/
https://www.ncbi.nlm.nih.gov/pubmed/29892541
http://dx.doi.org/10.1016/j.rmcr.2018.06.003
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