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Posterior fossa medulloblastoma in an atypical extra-axial location: A case report

Medulloblastoma is the most common posterior fossa tumor of childhood typically within the fourth ventricle. However, extra-axial medulloblastoma in posterior fossa is an uncommon diagnosis. We report a case in a 33-month-old male who presented with repeated complaints of abdominal pain, intermitten...

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Autores principales: Presutto, Elizabeth, Chappell, Matthew, Fullmer, Joseph, Ezhapilli, Sajeev
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5999935/
https://www.ncbi.nlm.nih.gov/pubmed/29904474
http://dx.doi.org/10.1016/j.radcr.2018.01.007
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author Presutto, Elizabeth
Chappell, Matthew
Fullmer, Joseph
Ezhapilli, Sajeev
author_facet Presutto, Elizabeth
Chappell, Matthew
Fullmer, Joseph
Ezhapilli, Sajeev
author_sort Presutto, Elizabeth
collection PubMed
description Medulloblastoma is the most common posterior fossa tumor of childhood typically within the fourth ventricle. However, extra-axial medulloblastoma in posterior fossa is an uncommon diagnosis. We report a case in a 33-month-old male who presented with repeated complaints of abdominal pain, intermittent emesis, and diarrhea, and diagnosed with right cerebellar extra-axial medulloblastoma, which was surgically resected. Majority of the reported extra-axial medulloblastoma in posterior fossa in the United States are located in the cerebellopontine angle. However, to the best of our knowledge, our case is the first to document medulloblastoma occurring exclusively in the cerebellar hemispheric extra-axial space rather than the cerebellopontine angle. Although the diagnosis can present as a radiological dilemma, a systematic multimodality imaging approach can aid in narrowing the differential diagnosis and timely management. In this case report, we will discuss the imaging characteristics, differential diagnosis, and management strategies, alongside a brief review of the world literature of extra-axial medulloblastoma.
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spelling pubmed-59999352018-06-14 Posterior fossa medulloblastoma in an atypical extra-axial location: A case report Presutto, Elizabeth Chappell, Matthew Fullmer, Joseph Ezhapilli, Sajeev Radiol Case Rep Neuroradiology Medulloblastoma is the most common posterior fossa tumor of childhood typically within the fourth ventricle. However, extra-axial medulloblastoma in posterior fossa is an uncommon diagnosis. We report a case in a 33-month-old male who presented with repeated complaints of abdominal pain, intermittent emesis, and diarrhea, and diagnosed with right cerebellar extra-axial medulloblastoma, which was surgically resected. Majority of the reported extra-axial medulloblastoma in posterior fossa in the United States are located in the cerebellopontine angle. However, to the best of our knowledge, our case is the first to document medulloblastoma occurring exclusively in the cerebellar hemispheric extra-axial space rather than the cerebellopontine angle. Although the diagnosis can present as a radiological dilemma, a systematic multimodality imaging approach can aid in narrowing the differential diagnosis and timely management. In this case report, we will discuss the imaging characteristics, differential diagnosis, and management strategies, alongside a brief review of the world literature of extra-axial medulloblastoma. Elsevier 2018-02-03 /pmc/articles/PMC5999935/ /pubmed/29904474 http://dx.doi.org/10.1016/j.radcr.2018.01.007 Text en © 2018 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Neuroradiology
Presutto, Elizabeth
Chappell, Matthew
Fullmer, Joseph
Ezhapilli, Sajeev
Posterior fossa medulloblastoma in an atypical extra-axial location: A case report
title Posterior fossa medulloblastoma in an atypical extra-axial location: A case report
title_full Posterior fossa medulloblastoma in an atypical extra-axial location: A case report
title_fullStr Posterior fossa medulloblastoma in an atypical extra-axial location: A case report
title_full_unstemmed Posterior fossa medulloblastoma in an atypical extra-axial location: A case report
title_short Posterior fossa medulloblastoma in an atypical extra-axial location: A case report
title_sort posterior fossa medulloblastoma in an atypical extra-axial location: a case report
topic Neuroradiology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5999935/
https://www.ncbi.nlm.nih.gov/pubmed/29904474
http://dx.doi.org/10.1016/j.radcr.2018.01.007
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