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Esophageal lung with rare associated vascular and anorectal malformations

Esophageal lung is a rare communicating bronchopulmonary foregut malformation in which the main bronchus arising from the trachea is absent. The affected lung is usually hypoplastic and aerated via an anomalous airway originating from the esophagus. Other anomalies such as esophageal atresia with tr...

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Autores principales: Alsaadi, Ali, Alsufiani, Hamdi A., Allugmani, Mohammad D., Gora, Altaf Hussain
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6000028/
https://www.ncbi.nlm.nih.gov/pubmed/29904493
http://dx.doi.org/10.1016/j.radcr.2018.01.029
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author Alsaadi, Ali
Alsufiani, Hamdi A.
Allugmani, Mohammad D.
Gora, Altaf Hussain
author_facet Alsaadi, Ali
Alsufiani, Hamdi A.
Allugmani, Mohammad D.
Gora, Altaf Hussain
author_sort Alsaadi, Ali
collection PubMed
description Esophageal lung is a rare communicating bronchopulmonary foregut malformation in which the main bronchus arising from the trachea is absent. The affected lung is usually hypoplastic and aerated via an anomalous airway originating from the esophagus. Other anomalies such as esophageal atresia with tracheoesophageal fistula or VACTERL (vertebral defects, anal atresia, cardiac defects, tracheoesophageal fistula, renal anomalies, and limb abnormalities) association can co-exist. The initial radiographic findings may be normal, but subsequent imaging usually shows progressive and recurrent lung collapse, probably because of recurrent aspiration through the anomalous airway and poor compliance of the affected lung during breathing. In this report, we describe a neonate with esophageal lung and rare associated anomalies, including anorectal malformation, pulmonary artery sling, and inferior vena cava interruption with azygous continuation. To our knowledge, this is the first report of esophageal lung with such associations.
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spelling pubmed-60000282018-06-14 Esophageal lung with rare associated vascular and anorectal malformations Alsaadi, Ali Alsufiani, Hamdi A. Allugmani, Mohammad D. Gora, Altaf Hussain Radiol Case Rep Pediatric Esophageal lung is a rare communicating bronchopulmonary foregut malformation in which the main bronchus arising from the trachea is absent. The affected lung is usually hypoplastic and aerated via an anomalous airway originating from the esophagus. Other anomalies such as esophageal atresia with tracheoesophageal fistula or VACTERL (vertebral defects, anal atresia, cardiac defects, tracheoesophageal fistula, renal anomalies, and limb abnormalities) association can co-exist. The initial radiographic findings may be normal, but subsequent imaging usually shows progressive and recurrent lung collapse, probably because of recurrent aspiration through the anomalous airway and poor compliance of the affected lung during breathing. In this report, we describe a neonate with esophageal lung and rare associated anomalies, including anorectal malformation, pulmonary artery sling, and inferior vena cava interruption with azygous continuation. To our knowledge, this is the first report of esophageal lung with such associations. Elsevier 2018-02-28 /pmc/articles/PMC6000028/ /pubmed/29904493 http://dx.doi.org/10.1016/j.radcr.2018.01.029 Text en © 2018 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Pediatric
Alsaadi, Ali
Alsufiani, Hamdi A.
Allugmani, Mohammad D.
Gora, Altaf Hussain
Esophageal lung with rare associated vascular and anorectal malformations
title Esophageal lung with rare associated vascular and anorectal malformations
title_full Esophageal lung with rare associated vascular and anorectal malformations
title_fullStr Esophageal lung with rare associated vascular and anorectal malformations
title_full_unstemmed Esophageal lung with rare associated vascular and anorectal malformations
title_short Esophageal lung with rare associated vascular and anorectal malformations
title_sort esophageal lung with rare associated vascular and anorectal malformations
topic Pediatric
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6000028/
https://www.ncbi.nlm.nih.gov/pubmed/29904493
http://dx.doi.org/10.1016/j.radcr.2018.01.029
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