Submacular sclerosing capillary hemangioblastoma

PURPOSE: To report a case of submacular cystic lesion that turned out to be a sclerosing capillary hemangioblastoma. The retinal capillary hemangioblastoma may arise as a part of von Hippel-Lindau syndrome (1) however, they may occur as an isolated entity (2), but submacular capillary hemangioblasto...

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Detalles Bibliográficos
Autores principales: Hamza, Hany S., Elhusseiny, Abdelrahman M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2018
Materias:
Brief report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6040628/
https://www.ncbi.nlm.nih.gov/pubmed/30003174
http://dx.doi.org/10.1016/j.ajoc.2018.05.010
Descripción
Sumario:PURPOSE: To report a case of submacular cystic lesion that turned out to be a sclerosing capillary hemangioblastoma. The retinal capillary hemangioblastoma may arise as a part of von Hippel-Lindau syndrome (1) however, they may occur as an isolated entity (2), but submacular capillary hemangioblastoma has never been reported. OBSERVATIONS: A case of a 56-year-old female who presented with a right yellow submacular lesion. The mass was excised via pars-plana vitrectomy and histopathological assessment revealed a submacular sclerosing capillary hemangioblastoma. CONCLUSION: and importance: The capillary hemangioblastoma is a benign vascular tumor that may arise submacularly and is not necessarily associated with von Hippel-Lindau disease. It is difficult to be differentiated clinically from other submacular lesions but the possibility should be considered.

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