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Fatal Postpartum Hemorrhage in a Patient with Niemann-Pick Disease Type B

BACKGROUND: Niemann-Pick Disease Type B (NPD B) is a rare lysosomal storage disorder resulting from an inherited deficiency of acid sphingomyelinase activity. Here, we report the case of a splenectomized patient with NPD B who died because of severe postpartum hemorrhage (PPH). CASE PRESENTATION: A...

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Detalles Bibliográficos
Autores principales:	Tanacan, Atakan, Yalcin, Abdullah, Unal, Canan, Akinci, Seda Banu, Beksac, Mehmet Sinan
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Hindawi 2018
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6046142/ https://www.ncbi.nlm.nih.gov/pubmed/30050708 http://dx.doi.org/10.1155/2018/9719374

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