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Revisiting transthyretin related cardiac amyloidosis: Case report and review of literature
Amyloidosis is a complex group of disorders that can involve many organs and cause their dysfunction. Cardiac involvement indicates worse prognosis and influences treatment strategies. Cardiac amyloidosis is an under-diagnosed entity and high index of clinical suspicion and careful interpretation of...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
PAGEPress Publications, Pavia, Italy
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6047478/ https://www.ncbi.nlm.nih.gov/pubmed/30069298 http://dx.doi.org/10.4081/cp.2018.1054 |
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author | Sharma, Munish Koman, Eduard Ledley, Gary S. Cho, Sung-Hae |
author_facet | Sharma, Munish Koman, Eduard Ledley, Gary S. Cho, Sung-Hae |
author_sort | Sharma, Munish |
collection | PubMed |
description | Amyloidosis is a complex group of disorders that can involve many organs and cause their dysfunction. Cardiac involvement indicates worse prognosis and influences treatment strategies. Cardiac amyloidosis is an under-diagnosed entity and high index of clinical suspicion and careful interpretation of basic diagnostic tools such as electrocardiogram and echocardiography is needed for early detection. Congestive heart failure due to restrictive pattern and/or conduction system abnormality, in absence of coronary artery disease should raise suspicion. We present a case of transthyretin related cardiac amyloidosis and discuss the key clinical and diagnostic findings along with review of existing literature regarding its management and outcomes. |
format | Online Article Text |
id | pubmed-6047478 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | PAGEPress Publications, Pavia, Italy |
record_format | MEDLINE/PubMed |
spelling | pubmed-60474782018-08-01 Revisiting transthyretin related cardiac amyloidosis: Case report and review of literature Sharma, Munish Koman, Eduard Ledley, Gary S. Cho, Sung-Hae Clin Pract Case Report Amyloidosis is a complex group of disorders that can involve many organs and cause their dysfunction. Cardiac involvement indicates worse prognosis and influences treatment strategies. Cardiac amyloidosis is an under-diagnosed entity and high index of clinical suspicion and careful interpretation of basic diagnostic tools such as electrocardiogram and echocardiography is needed for early detection. Congestive heart failure due to restrictive pattern and/or conduction system abnormality, in absence of coronary artery disease should raise suspicion. We present a case of transthyretin related cardiac amyloidosis and discuss the key clinical and diagnostic findings along with review of existing literature regarding its management and outcomes. PAGEPress Publications, Pavia, Italy 2018-05-16 /pmc/articles/PMC6047478/ /pubmed/30069298 http://dx.doi.org/10.4081/cp.2018.1054 Text en ©Copyright M. Sharma et al., 2018 http://creativecommons.org/licenses/by-nc/4.0/ This work is licensed under a Creative Commons Attribution NonCommercial 4.0 License (CC BY-NC 4.0). |
spellingShingle | Case Report Sharma, Munish Koman, Eduard Ledley, Gary S. Cho, Sung-Hae Revisiting transthyretin related cardiac amyloidosis: Case report and review of literature |
title | Revisiting transthyretin related cardiac amyloidosis: Case report and review of literature |
title_full | Revisiting transthyretin related cardiac amyloidosis: Case report and review of literature |
title_fullStr | Revisiting transthyretin related cardiac amyloidosis: Case report and review of literature |
title_full_unstemmed | Revisiting transthyretin related cardiac amyloidosis: Case report and review of literature |
title_short | Revisiting transthyretin related cardiac amyloidosis: Case report and review of literature |
title_sort | revisiting transthyretin related cardiac amyloidosis: case report and review of literature |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6047478/ https://www.ncbi.nlm.nih.gov/pubmed/30069298 http://dx.doi.org/10.4081/cp.2018.1054 |
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