Cargando…
Solitary mastocytoma presenting at birth
Mastocytosis is a rare disease which occurs in both children and adults, and it can manifest as a solitary or multiple skin lesions. Both can cause cutaneous or systemic symptoms. Because of the heterogeneity of clinical presentation of mastocytosis and its rare prevalence, it can be hard to suspect...
Autores principales: | , , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Korean Cleft Palate-Craniofacial Association
2018
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6057127/ https://www.ncbi.nlm.nih.gov/pubmed/29716178 http://dx.doi.org/10.7181/acfs.2018.01508 |
_version_ | 1783341465443762176 |
---|---|
author | Ha, Non Hyeon Lee, Yoo Jung Park, Myong Chul Lee, Il Jae Kim, Sue Min Park, Dong Ha |
author_facet | Ha, Non Hyeon Lee, Yoo Jung Park, Myong Chul Lee, Il Jae Kim, Sue Min Park, Dong Ha |
author_sort | Ha, Non Hyeon |
collection | PubMed |
description | Mastocytosis is a rare disease which occurs in both children and adults, and it can manifest as a solitary or multiple skin lesions. Both can cause cutaneous or systemic symptoms. Because of the heterogeneity of clinical presentation of mastocytosis and its rare prevalence, it can be hard to suspect the mastocytosis at the first time. Most solitary mastocytomas are about 1–5 cm in diameter and have features of brownish-yellow, minimally elevated plaques with a smooth shiny surface. This article presents a case of solitary mastocytoma which occurred in neonate and that we treated through surgical excision. In histopathological examination, it consisted of c-kit-positive mast cells. Although pediatric cutaneous mastocytosis might regress spontaneously, clinicians should keep in mind that it could be associated with systemic mastocytosis which involves hematopoietic system. |
format | Online Article Text |
id | pubmed-6057127 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | Korean Cleft Palate-Craniofacial Association |
record_format | MEDLINE/PubMed |
spelling | pubmed-60571272018-07-27 Solitary mastocytoma presenting at birth Ha, Non Hyeon Lee, Yoo Jung Park, Myong Chul Lee, Il Jae Kim, Sue Min Park, Dong Ha Arch Craniofac Surg Case Report Mastocytosis is a rare disease which occurs in both children and adults, and it can manifest as a solitary or multiple skin lesions. Both can cause cutaneous or systemic symptoms. Because of the heterogeneity of clinical presentation of mastocytosis and its rare prevalence, it can be hard to suspect the mastocytosis at the first time. Most solitary mastocytomas are about 1–5 cm in diameter and have features of brownish-yellow, minimally elevated plaques with a smooth shiny surface. This article presents a case of solitary mastocytoma which occurred in neonate and that we treated through surgical excision. In histopathological examination, it consisted of c-kit-positive mast cells. Although pediatric cutaneous mastocytosis might regress spontaneously, clinicians should keep in mind that it could be associated with systemic mastocytosis which involves hematopoietic system. Korean Cleft Palate-Craniofacial Association 2018-06 2018-04-28 /pmc/articles/PMC6057127/ /pubmed/29716178 http://dx.doi.org/10.7181/acfs.2018.01508 Text en Copyright © 2018 The Korean Cleft Palate-Craniofacial Association https://creativecommons.org/licenses/by-nc/4.0/This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/ (https://creativecommons.org/licenses/by-nc/4.0/) ) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Ha, Non Hyeon Lee, Yoo Jung Park, Myong Chul Lee, Il Jae Kim, Sue Min Park, Dong Ha Solitary mastocytoma presenting at birth |
title | Solitary mastocytoma presenting at birth |
title_full | Solitary mastocytoma presenting at birth |
title_fullStr | Solitary mastocytoma presenting at birth |
title_full_unstemmed | Solitary mastocytoma presenting at birth |
title_short | Solitary mastocytoma presenting at birth |
title_sort | solitary mastocytoma presenting at birth |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6057127/ https://www.ncbi.nlm.nih.gov/pubmed/29716178 http://dx.doi.org/10.7181/acfs.2018.01508 |
work_keys_str_mv | AT hanonhyeon solitarymastocytomapresentingatbirth AT leeyoojung solitarymastocytomapresentingatbirth AT parkmyongchul solitarymastocytomapresentingatbirth AT leeiljae solitarymastocytomapresentingatbirth AT kimsuemin solitarymastocytomapresentingatbirth AT parkdongha solitarymastocytomapresentingatbirth |