Le cholédococèle: une variété rare de dilatation kystique congénitale des voies biliaires

Cystic dilation of the bile ducts (CDBD) is a rare disease in which pain is the major symptom. It mainly affects young women. Carcinogenesis is the main risk of this disease. Complete surgical resection is the treatment of choice. TODANI's classification defines five groups of congenital cystic dilatation of the bile ducts. Choledochocele is classi?ed as type III and is defined as an isolated cystic dilation of the ampulla of Vater. Few studies were published in the literature due to its rarity and to its multitude of clinical presentations. The lack of guidelines resulted in approaches to treatment based on endoscopic treatment, making rapid progress but considered as a conservative option, or on hardly obtainable complete surgical resection. This study reports the case of a 32-year old female patient presenting with cyclic epigastric pain. Morpho-clinical examinations showed holedochocele. Complete resection of the cyst via duodenotomy with reimplantation of the common bile duct and of the Wirsung duct associated with cholecystectomy were performed.