Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease

The authors present a classic case of Churg-Strauss syndrome with an exuberant clinical picture in a 34-year-old woman. She showed the following diagnostic criteria: asthma, polyneuropathy, rhinopathy, marked eosinophilia, positive p-ANCA with a perinuclear pattern, and skin histopathology results s...

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Autores principales: Mukamal, Luana Vieira, Sodré, Celso Tavares, Prata, Lara Beatriz, Nakasato, Fernanda, Cuzzi, Tullia, Ramos-e-Silva, Marcia
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2018
Materias:
Single Case
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6062663/
https://www.ncbi.nlm.nih.gov/pubmed/30057533
http://dx.doi.org/10.1159/000489162
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author Mukamal, Luana Vieira
Sodré, Celso Tavares
Prata, Lara Beatriz
Nakasato, Fernanda
Cuzzi, Tullia
Ramos-e-Silva, Marcia
author_facet Mukamal, Luana Vieira
Sodré, Celso Tavares
Prata, Lara Beatriz
Nakasato, Fernanda
Cuzzi, Tullia
Ramos-e-Silva, Marcia
author_sort Mukamal, Luana Vieira
collection PubMed
description The authors present a classic case of Churg-Strauss syndrome with an exuberant clinical picture in a 34-year-old woman. She showed the following diagnostic criteria: asthma, polyneuropathy, rhinopathy, marked eosinophilia, positive p-ANCA with a perinuclear pattern, and skin histopathology results suggestive of vasculitis with eosinophils. There was a good response to prednisone, dexamethasone pulse therapy, and cyclophosphamide.
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spelling pubmed-60626632018-07-27 Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease Mukamal, Luana Vieira Sodré, Celso Tavares Prata, Lara Beatriz Nakasato, Fernanda Cuzzi, Tullia Ramos-e-Silva, Marcia Case Rep Dermatol Single Case The authors present a classic case of Churg-Strauss syndrome with an exuberant clinical picture in a 34-year-old woman. She showed the following diagnostic criteria: asthma, polyneuropathy, rhinopathy, marked eosinophilia, positive p-ANCA with a perinuclear pattern, and skin histopathology results suggestive of vasculitis with eosinophils. There was a good response to prednisone, dexamethasone pulse therapy, and cyclophosphamide. S. Karger AG 2018-06-29 /pmc/articles/PMC6062663/ /pubmed/30057533 http://dx.doi.org/10.1159/000489162 Text en Copyright © 2018 by S. Karger AG, Basel http://creativecommons.org/licenses/by-nc/4.0/ This article is licensed under the Creative Commons Attribution-NonCommercial-4.0 International License (CC BY-NC) (http://www.karger.com/Services/OpenAccessLicense). Usage and distribution for commercial purposes requires written permission.
spellingShingle Single Case
Mukamal, Luana Vieira
Sodré, Celso Tavares
Prata, Lara Beatriz
Nakasato, Fernanda
Cuzzi, Tullia
Ramos-e-Silva, Marcia
Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title_full Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title_fullStr Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title_full_unstemmed Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title_short Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title_sort churg-strauss syndrome or eosinophilic granulomatosis with polyangiitis: exuberant classic clinical picture of a rare disease
topic Single Case
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6062663/
https://www.ncbi.nlm.nih.gov/pubmed/30057533
http://dx.doi.org/10.1159/000489162
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