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Characterization of Drosophila ATPsynC mutants as a new model of mitochondrial ATP synthase disorders

Mitochondrial disorders associated with genetic defects of the ATP synthase are among the most deleterious diseases of the neuromuscular system that primarily manifest in newborns. Nevertheless, the number of established animal models for the elucidation of the molecular mechanisms behind such patho...

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Detalles Bibliográficos
Autores principales:	Lovero, Domenica, Giordano, Luca, Marsano, René Massimiliano, Sanchez-Martinez, Alvaro, Boukhatmi, Hadi, Drechsler, Maik, Oliva, Marta, Whitworth, Alexander J., Porcelli, Damiano, Caggese, Corrado
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2018
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6086398/ https://www.ncbi.nlm.nih.gov/pubmed/30096161 http://dx.doi.org/10.1371/journal.pone.0201811

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