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Anesthesia Management of Vitrectomy in a Patient with Sturge-Weber Syndrome
Sturge-Weber syndrome (SWS) is a neurocutaneous disorder, characterized by leptomeningeal angiomas involving the oral cavity, trachea, larynx, and face. Herein, we present a case of vitrectomy in a seven-year-old boy with SWS. The patient showed hemangioma on the left side of his face, as well as me...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
National Research Institute of Tuberculosis and Lung Disease
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6087527/ https://www.ncbi.nlm.nih.gov/pubmed/30116281 |
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author | Roodneshin, Fatemeh Poor Zamany Nejat Kermany, Mahtab Rostami, Pooya Tanghatari, Hamed |
author_facet | Roodneshin, Fatemeh Poor Zamany Nejat Kermany, Mahtab Rostami, Pooya Tanghatari, Hamed |
author_sort | Roodneshin, Fatemeh |
collection | PubMed |
description | Sturge-Weber syndrome (SWS) is a neurocutaneous disorder, characterized by leptomeningeal angiomas involving the oral cavity, trachea, larynx, and face. Herein, we present a case of vitrectomy in a seven-year-old boy with SWS. The patient showed hemangioma on the left side of his face, as well as mental retardation and epilepsy. Preoperative examination revealed no apparent hemangioma in the oral cavity, pharynx, larynx, or trachea. However, he was predicted to have difficult airway intubation, as the oral cavity was smaller than the normal size. The minimum Mallampati score was 3–4 due to macroglossia. First, we applied awake intubation, but he failed to follow the commands. We proceeded to general anesthesia with propofol and did not use any muscle relaxants to maintain spontaneous breathing. A laryngeal mask airway was inserted to minimize any harm to possible oral angiomas. The patient was hemodynamically stable and extubated without any complications, such as bleeding or respiratory problems. |
format | Online Article Text |
id | pubmed-6087527 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | National Research Institute of Tuberculosis and Lung Disease |
record_format | MEDLINE/PubMed |
spelling | pubmed-60875272018-08-16 Anesthesia Management of Vitrectomy in a Patient with Sturge-Weber Syndrome Roodneshin, Fatemeh Poor Zamany Nejat Kermany, Mahtab Rostami, Pooya Tanghatari, Hamed Tanaffos Case Report Sturge-Weber syndrome (SWS) is a neurocutaneous disorder, characterized by leptomeningeal angiomas involving the oral cavity, trachea, larynx, and face. Herein, we present a case of vitrectomy in a seven-year-old boy with SWS. The patient showed hemangioma on the left side of his face, as well as mental retardation and epilepsy. Preoperative examination revealed no apparent hemangioma in the oral cavity, pharynx, larynx, or trachea. However, he was predicted to have difficult airway intubation, as the oral cavity was smaller than the normal size. The minimum Mallampati score was 3–4 due to macroglossia. First, we applied awake intubation, but he failed to follow the commands. We proceeded to general anesthesia with propofol and did not use any muscle relaxants to maintain spontaneous breathing. A laryngeal mask airway was inserted to minimize any harm to possible oral angiomas. The patient was hemodynamically stable and extubated without any complications, such as bleeding or respiratory problems. National Research Institute of Tuberculosis and Lung Disease 2018-01 /pmc/articles/PMC6087527/ /pubmed/30116281 Text en Copyright© 2018 National Research Institute of Tuberculosis and Lung Disease http://creativecommons.org/licenses/by/3.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Roodneshin, Fatemeh Poor Zamany Nejat Kermany, Mahtab Rostami, Pooya Tanghatari, Hamed Anesthesia Management of Vitrectomy in a Patient with Sturge-Weber Syndrome |
title | Anesthesia Management of Vitrectomy in a Patient with Sturge-Weber Syndrome |
title_full | Anesthesia Management of Vitrectomy in a Patient with Sturge-Weber Syndrome |
title_fullStr | Anesthesia Management of Vitrectomy in a Patient with Sturge-Weber Syndrome |
title_full_unstemmed | Anesthesia Management of Vitrectomy in a Patient with Sturge-Weber Syndrome |
title_short | Anesthesia Management of Vitrectomy in a Patient with Sturge-Weber Syndrome |
title_sort | anesthesia management of vitrectomy in a patient with sturge-weber syndrome |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6087527/ https://www.ncbi.nlm.nih.gov/pubmed/30116281 |
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