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Alveolar capillary dysplasia with misalignment of the pulmonary veins: clinical, histological, and genetic aspects

Alveolar capillary dysplasia with misalignment of the pulmonary veins (ACD/MPV) is a rare and lethal disorder mainly involving the vascular development of the lungs. Since its first description, significant achievements in research have led to a better understanding of the underlying molecular mecha...

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Detalles Bibliográficos
Autores principales:	Slot, Evelien, Edel, Gabriëla, Cutz, Ernest, van Heijst, Arno, Post, Martin, Schnater, Marco, Wijnen, René, Tibboel, Dick, Rottier, Robbert, de Klein, Annelies
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	SAGE Publications 2018
Materias:	Review Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6108021/ https://www.ncbi.nlm.nih.gov/pubmed/30058937 http://dx.doi.org/10.1177/2045894018795143

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