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Oral Tongue Malignancies in Autoimmune Polyendocrine Syndrome Type 1
Autoimmune polyendocrinopathy-candidiasis-ectodermal dystrophy (APECED) or Autoimmune polyendocrine syndrome type-1 (APS-1) (APECED, OMIM 240300) is a rare, childhood onset, monogenic disease caused by mutations in the Autoimmune Regulator (AIRE) gene. The overall mortality is increased compared to...
Autores principales: | Bruserud, Øyvind, Costea, Daniela-Elena, Laakso, Saila, Garty, Ben-Zion, Mathisen, Eirik, Mäkitie, Antti, Mäkitie, Outi, Husebye, Eystein S. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6109689/ https://www.ncbi.nlm.nih.gov/pubmed/30177913 http://dx.doi.org/10.3389/fendo.2018.00463 |
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