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Systematic Review: The Epidemiology, Natural History, and Burden of Alagille Syndrome

BACKGROUND AND AIM: Alagille syndrome (ALGS) is an inherited multisystem disorder typically manifesting as cholestasis, and potentially leading to end-stage liver disease and death. The aim of the study was to perform the first systematic review of the epidemiology, natural history, and burden of AL...

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Detalles Bibliográficos
Autores principales:	Kamath, Binita M., Baker, Alastair, Houwen, Roderick, Todorova, Lora, Kerkar, Nanda
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Lippincott Williams & Wilkins 2018
Materias:	Invited Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6110620/ https://www.ncbi.nlm.nih.gov/pubmed/29543694 http://dx.doi.org/10.1097/MPG.0000000000001958

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