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Mesenteric fibromatosis in a patient with a history of neuroblastoma: a case report

Mesenteric fibromatosis (MF) is a locally aggressive proliferative spindle cell lesion of the mesentery. A 34-year-old male presented with increasing abdominal pain and constipation. On workup, patient was found to have a large pelvic mass on CT A/P concerning for cancer. The patient underwent surgi...

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Autores principales: Abate, Miseker, Pigazzi, Alessio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6119216/
https://www.ncbi.nlm.nih.gov/pubmed/30186589
http://dx.doi.org/10.1093/jscr/rjy209
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author Abate, Miseker
Pigazzi, Alessio
author_facet Abate, Miseker
Pigazzi, Alessio
author_sort Abate, Miseker
collection PubMed
description Mesenteric fibromatosis (MF) is a locally aggressive proliferative spindle cell lesion of the mesentery. A 34-year-old male presented with increasing abdominal pain and constipation. On workup, patient was found to have a large pelvic mass on CT A/P concerning for cancer. The patient underwent surgical excision of >15 cm intra-abdominal tumor along with adherent small bowel section. Histology of the tumor showed a spindle cell lesion consistent with MF. Previous reports have shown association of MF with Gardner syndrome and familial adenomatous polyposis. We present the first reported case of MF in a patient with previous neuroblastoma.
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spelling pubmed-61192162018-09-05 Mesenteric fibromatosis in a patient with a history of neuroblastoma: a case report Abate, Miseker Pigazzi, Alessio J Surg Case Rep Case Report Mesenteric fibromatosis (MF) is a locally aggressive proliferative spindle cell lesion of the mesentery. A 34-year-old male presented with increasing abdominal pain and constipation. On workup, patient was found to have a large pelvic mass on CT A/P concerning for cancer. The patient underwent surgical excision of >15 cm intra-abdominal tumor along with adherent small bowel section. Histology of the tumor showed a spindle cell lesion consistent with MF. Previous reports have shown association of MF with Gardner syndrome and familial adenomatous polyposis. We present the first reported case of MF in a patient with previous neuroblastoma. Oxford University Press 2018-09-01 /pmc/articles/PMC6119216/ /pubmed/30186589 http://dx.doi.org/10.1093/jscr/rjy209 Text en Published by Oxford University Press and JSCR Publishing Ltd. All rights reserved. © The Author(s) 2018. http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com
spellingShingle Case Report
Abate, Miseker
Pigazzi, Alessio
Mesenteric fibromatosis in a patient with a history of neuroblastoma: a case report
title Mesenteric fibromatosis in a patient with a history of neuroblastoma: a case report
title_full Mesenteric fibromatosis in a patient with a history of neuroblastoma: a case report
title_fullStr Mesenteric fibromatosis in a patient with a history of neuroblastoma: a case report
title_full_unstemmed Mesenteric fibromatosis in a patient with a history of neuroblastoma: a case report
title_short Mesenteric fibromatosis in a patient with a history of neuroblastoma: a case report
title_sort mesenteric fibromatosis in a patient with a history of neuroblastoma: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6119216/
https://www.ncbi.nlm.nih.gov/pubmed/30186589
http://dx.doi.org/10.1093/jscr/rjy209
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