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Patient-Derived Stem Cell Models in SPAST HSP: Disease Modelling and Drug Discovery
Hereditary spastic paraplegia is an inherited, progressive paralysis of the lower limbs first described by Adolph Strümpell in 1883 with a further detailed description of the disease by Maurice Lorrain in 1888. Today, more than 100 years after the first case of HSP was described, we still do not kno...
Autores principales: | Wali, Gautam, Sue, Carolyn M., Mackay-Sim, Alan |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6120041/ https://www.ncbi.nlm.nih.gov/pubmed/30065201 http://dx.doi.org/10.3390/brainsci8080142 |
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