A Long-Term Survivor with Tetralogy of Fallot Treated Only with the Classical Blalock-Taussig Shunt

The prognosis of tetralogy of Fallot (TOF) treated only with Blalock-Taussig shunt (BTS) operation is unclear. A woman with TOF underwent classic BTS operation at 10 years of age. Despite no medication, she delivered two children and worked without apparent heart failure. At 72 years of age, she com...

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Autores principales: Yamada, Yu, Ishizu, Tomoko, Tsuneoka, Hidekazu, Eki, Yutaka, Horigome, Hitoshi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2018
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6120336/
https://www.ncbi.nlm.nih.gov/pubmed/30210878
http://dx.doi.org/10.1155/2018/5262745
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author Yamada, Yu
Ishizu, Tomoko
Tsuneoka, Hidekazu
Eki, Yutaka
Horigome, Hitoshi
author_facet Yamada, Yu
Ishizu, Tomoko
Tsuneoka, Hidekazu
Eki, Yutaka
Horigome, Hitoshi
author_sort Yamada, Yu
collection PubMed
description The prognosis of tetralogy of Fallot (TOF) treated only with Blalock-Taussig shunt (BTS) operation is unclear. A woman with TOF underwent classic BTS operation at 10 years of age. Despite no medication, she delivered two children and worked without apparent heart failure. At 72 years of age, she complained of dyspnea on exertion and leg edema. The cardiac angiogram revealed a well-patent BTS and severely stenotic right ventricular outflow tract. Right heart catheterization showed adequately maintained pulmonary blood flow with slight pulmonary arterial hypertension. Her unexpected yet favorable outcome reaffirms the importance of structural and functional self-adaptation even with cyanosis. If she had undergone a valve-sparing corrective surgery in adolescence, much better quality of life and outcome could have been expected.
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spelling pubmed-61203362018-09-12 A Long-Term Survivor with Tetralogy of Fallot Treated Only with the Classical Blalock-Taussig Shunt Yamada, Yu Ishizu, Tomoko Tsuneoka, Hidekazu Eki, Yutaka Horigome, Hitoshi Case Rep Cardiol Case Report The prognosis of tetralogy of Fallot (TOF) treated only with Blalock-Taussig shunt (BTS) operation is unclear. A woman with TOF underwent classic BTS operation at 10 years of age. Despite no medication, she delivered two children and worked without apparent heart failure. At 72 years of age, she complained of dyspnea on exertion and leg edema. The cardiac angiogram revealed a well-patent BTS and severely stenotic right ventricular outflow tract. Right heart catheterization showed adequately maintained pulmonary blood flow with slight pulmonary arterial hypertension. Her unexpected yet favorable outcome reaffirms the importance of structural and functional self-adaptation even with cyanosis. If she had undergone a valve-sparing corrective surgery in adolescence, much better quality of life and outcome could have been expected. Hindawi 2018-08-19 /pmc/articles/PMC6120336/ /pubmed/30210878 http://dx.doi.org/10.1155/2018/5262745 Text en Copyright © 2018 Yu Yamada et al. http://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Yamada, Yu
Ishizu, Tomoko
Tsuneoka, Hidekazu
Eki, Yutaka
Horigome, Hitoshi
A Long-Term Survivor with Tetralogy of Fallot Treated Only with the Classical Blalock-Taussig Shunt
title A Long-Term Survivor with Tetralogy of Fallot Treated Only with the Classical Blalock-Taussig Shunt
title_full A Long-Term Survivor with Tetralogy of Fallot Treated Only with the Classical Blalock-Taussig Shunt
title_fullStr A Long-Term Survivor with Tetralogy of Fallot Treated Only with the Classical Blalock-Taussig Shunt
title_full_unstemmed A Long-Term Survivor with Tetralogy of Fallot Treated Only with the Classical Blalock-Taussig Shunt
title_short A Long-Term Survivor with Tetralogy of Fallot Treated Only with the Classical Blalock-Taussig Shunt
title_sort long-term survivor with tetralogy of fallot treated only with the classical blalock-taussig shunt
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6120336/
https://www.ncbi.nlm.nih.gov/pubmed/30210878
http://dx.doi.org/10.1155/2018/5262745
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