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Integrative effects of dystrophin loss on metabolic function of the mdx mouse
Duchenne muscular dystrophy (DMD) is a disease marked by the development of skeletal muscle weakness and wasting. DMD results from mutations in the gene for the cytoskeletal protein dystrophin. The loss of dystrophin expression is not limited to muscle weakness but has multiple systemic consequences...
Autores principales: | Strakova, Jana, Kamdar, Forum, Kulhanek, Debra, Razzoli, Maria, Garry, Daniel J., Ervasti, James M., Bartolomucci, Alessandro, Townsend, DeWayne |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Nature Publishing Group UK
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6134145/ https://www.ncbi.nlm.nih.gov/pubmed/30206270 http://dx.doi.org/10.1038/s41598-018-31753-3 |
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