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Treatment of Granulomas in Patients With Ataxia Telangiectasia

Background: Ataxia telangiectasia (A-T) is a devastating multi-system disorder characterized by progressive cerebellar ataxia, growth retardation, immunodeficiency, chronic pulmonary disease and chromosomal instability. Cutaneous granulomas are a known phenomenon in A-T but extra-dermal manifestatio...

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Detalles Bibliográficos
Autores principales:	Woelke, Sandra, Valesky, Eva, Bakhtiar, Shahrzad, Pommerening, Helena, Pfeffermann, L. M., Schubert, Ralf, Zielen, Stefan
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2018
Materias:	Immunology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6153364/ https://www.ncbi.nlm.nih.gov/pubmed/30279689 http://dx.doi.org/10.3389/fimmu.2018.02000

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