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Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults—case report and review of the relevant literature
The Abernethy malformation consists of a congenital extrahepatic portosystemic shunt and is believed to be extremely rare in humans. The potential implications of abnormal portovenous shunting and decreased hepatic portal flow are numerous and potentially serious. Although congenital extrahepatic po...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The British Institute of Radiology
2017
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6159114/ https://www.ncbi.nlm.nih.gov/pubmed/30363163 http://dx.doi.org/10.1259/bjrcr.20170054 |
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author | Mesquita, Romeu Duarte Sousa, Marta Vilaverde, Filipa Cardoso, Rosa |
author_facet | Mesquita, Romeu Duarte Sousa, Marta Vilaverde, Filipa Cardoso, Rosa |
author_sort | Mesquita, Romeu Duarte |
collection | PubMed |
description | The Abernethy malformation consists of a congenital extrahepatic portosystemic shunt and is believed to be extremely rare in humans. The potential implications of abnormal portovenous shunting and decreased hepatic portal flow are numerous and potentially serious. Although congenital extrahepatic portosystemic shunts are increasingly suspected and diagnosed in specialized centres, much of their clinical presentation and natural history is not fully understood. Symptoms of portosystemic shunt are mainly caused by increased levels of ammonia, which lead to signs of encephalopathy. Therapeutic options depend on the type of shunt and its clinical course, so the classification of the congenital portosystemic shunt is a key finding in these patients. |
format | Online Article Text |
id | pubmed-6159114 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | The British Institute of Radiology |
record_format | MEDLINE/PubMed |
spelling | pubmed-61591142018-10-25 Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults—case report and review of the relevant literature Mesquita, Romeu Duarte Sousa, Marta Vilaverde, Filipa Cardoso, Rosa BJR Case Rep Case Report The Abernethy malformation consists of a congenital extrahepatic portosystemic shunt and is believed to be extremely rare in humans. The potential implications of abnormal portovenous shunting and decreased hepatic portal flow are numerous and potentially serious. Although congenital extrahepatic portosystemic shunts are increasingly suspected and diagnosed in specialized centres, much of their clinical presentation and natural history is not fully understood. Symptoms of portosystemic shunt are mainly caused by increased levels of ammonia, which lead to signs of encephalopathy. Therapeutic options depend on the type of shunt and its clinical course, so the classification of the congenital portosystemic shunt is a key finding in these patients. The British Institute of Radiology 2017-11-16 /pmc/articles/PMC6159114/ /pubmed/30363163 http://dx.doi.org/10.1259/bjrcr.20170054 Text en © 2017 The Authors. Published by the British Institute of Radiology http://creativecommons.org/licenses/by/4.0/ This is an open access article under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/) , which permits unrestricted use, distribution and reproduction in any medium, provided the original author and source are credited. |
spellingShingle | Case Report Mesquita, Romeu Duarte Sousa, Marta Vilaverde, Filipa Cardoso, Rosa Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults—case report and review of the relevant literature |
title | Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults—case report and review of the relevant literature |
title_full | Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults—case report and review of the relevant literature |
title_fullStr | Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults—case report and review of the relevant literature |
title_full_unstemmed | Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults—case report and review of the relevant literature |
title_short | Abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults—case report and review of the relevant literature |
title_sort | abernethy malformation: beware in cases of unexplained hepatic encephalopathy in adults—case report and review of the relevant literature |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6159114/ https://www.ncbi.nlm.nih.gov/pubmed/30363163 http://dx.doi.org/10.1259/bjrcr.20170054 |
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