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A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome
Adult intussusception is rare and is almost always associated with a lead point. Polyposis syndromes are a common cause of adult intussusceptions, with polyps acting as lead points. Peutz–Jeghers syndrome is associated with benign hamartomatous polyps and mucocutaneous pigmentation. Although hamarto...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The British Institute of Radiology
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6159284/ https://www.ncbi.nlm.nih.gov/pubmed/30363296 http://dx.doi.org/10.1259/bjrcr.20150314 |
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author | Panta, Om Biju Maharjan, Santosh Manandhar, Sujan Paudel, Sharma Ghimire, Ram Kumar |
author_facet | Panta, Om Biju Maharjan, Santosh Manandhar, Sujan Paudel, Sharma Ghimire, Ram Kumar |
author_sort | Panta, Om Biju |
collection | PubMed |
description | Adult intussusception is rare and is almost always associated with a lead point. Polyposis syndromes are a common cause of adult intussusceptions, with polyps acting as lead points. Peutz–Jeghers syndrome is associated with benign hamartomatous polyps and mucocutaneous pigmentation. Although hamartomatous polyps are not premalignant, there is an increased risk of gastrointestinal and non-gastrointestinal malignancy, most commonly involving the small bowel. Most patients with Peutz–Jeghers syndrome with acute abdomen are diagnosed to have intussusceptions, mostly of the enteroenteric type. Colocolic intussusceptions are rare in Peutz–Jeghers syndrome. To the best of our knowledge, synchronous colocolic intussusception in association with Peutz–Jeghers syndrome has not been previously reported. Here we present a case of malignant jejunal mass and synchronous colocolic intussusceptions in a patient with Peutz–Jeghers syndrome. |
format | Online Article Text |
id | pubmed-6159284 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | The British Institute of Radiology |
record_format | MEDLINE/PubMed |
spelling | pubmed-61592842018-10-25 A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome Panta, Om Biju Maharjan, Santosh Manandhar, Sujan Paudel, Sharma Ghimire, Ram Kumar BJR Case Rep Case Report Adult intussusception is rare and is almost always associated with a lead point. Polyposis syndromes are a common cause of adult intussusceptions, with polyps acting as lead points. Peutz–Jeghers syndrome is associated with benign hamartomatous polyps and mucocutaneous pigmentation. Although hamartomatous polyps are not premalignant, there is an increased risk of gastrointestinal and non-gastrointestinal malignancy, most commonly involving the small bowel. Most patients with Peutz–Jeghers syndrome with acute abdomen are diagnosed to have intussusceptions, mostly of the enteroenteric type. Colocolic intussusceptions are rare in Peutz–Jeghers syndrome. To the best of our knowledge, synchronous colocolic intussusception in association with Peutz–Jeghers syndrome has not been previously reported. Here we present a case of malignant jejunal mass and synchronous colocolic intussusceptions in a patient with Peutz–Jeghers syndrome. The British Institute of Radiology 2016-07-25 /pmc/articles/PMC6159284/ /pubmed/30363296 http://dx.doi.org/10.1259/bjrcr.20150314 Text en © 2017 The Authors. Published by the British Institute of Radiology http://creativecommons.org/licenses/by/4.0/ This is an open access article under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/) , which permits unrestricted use, distribution and reproduction in any medium, provided the original author and source are credited. |
spellingShingle | Case Report Panta, Om Biju Maharjan, Santosh Manandhar, Sujan Paudel, Sharma Ghimire, Ram Kumar A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome |
title | A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome |
title_full | A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome |
title_fullStr | A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome |
title_full_unstemmed | A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome |
title_short | A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome |
title_sort | rare case of synchronous colocolic intussusception in association with peutz–jeghers syndrome |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6159284/ https://www.ncbi.nlm.nih.gov/pubmed/30363296 http://dx.doi.org/10.1259/bjrcr.20150314 |
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