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A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome

Adult intussusception is rare and is almost always associated with a lead point. Polyposis syndromes are a common cause of adult intussusceptions, with polyps acting as lead points. Peutz–Jeghers syndrome is associated with benign hamartomatous polyps and mucocutaneous pigmentation. Although hamarto...

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Autores principales: Panta, Om Biju, Maharjan, Santosh, Manandhar, Sujan, Paudel, Sharma, Ghimire, Ram Kumar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The British Institute of Radiology 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6159284/
https://www.ncbi.nlm.nih.gov/pubmed/30363296
http://dx.doi.org/10.1259/bjrcr.20150314
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author Panta, Om Biju
Maharjan, Santosh
Manandhar, Sujan
Paudel, Sharma
Ghimire, Ram Kumar
author_facet Panta, Om Biju
Maharjan, Santosh
Manandhar, Sujan
Paudel, Sharma
Ghimire, Ram Kumar
author_sort Panta, Om Biju
collection PubMed
description Adult intussusception is rare and is almost always associated with a lead point. Polyposis syndromes are a common cause of adult intussusceptions, with polyps acting as lead points. Peutz–Jeghers syndrome is associated with benign hamartomatous polyps and mucocutaneous pigmentation. Although hamartomatous polyps are not premalignant, there is an increased risk of gastrointestinal and non-gastrointestinal malignancy, most commonly involving the small bowel. Most patients with Peutz–Jeghers syndrome with acute abdomen are diagnosed to have intussusceptions, mostly of the enteroenteric type. Colocolic intussusceptions are rare in Peutz–Jeghers syndrome. To the best of our knowledge, synchronous colocolic intussusception in association with Peutz–Jeghers syndrome has not been previously reported. Here we present a case of malignant jejunal mass and synchronous colocolic intussusceptions in a patient with Peutz–Jeghers syndrome.
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spelling pubmed-61592842018-10-25 A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome Panta, Om Biju Maharjan, Santosh Manandhar, Sujan Paudel, Sharma Ghimire, Ram Kumar BJR Case Rep Case Report Adult intussusception is rare and is almost always associated with a lead point. Polyposis syndromes are a common cause of adult intussusceptions, with polyps acting as lead points. Peutz–Jeghers syndrome is associated with benign hamartomatous polyps and mucocutaneous pigmentation. Although hamartomatous polyps are not premalignant, there is an increased risk of gastrointestinal and non-gastrointestinal malignancy, most commonly involving the small bowel. Most patients with Peutz–Jeghers syndrome with acute abdomen are diagnosed to have intussusceptions, mostly of the enteroenteric type. Colocolic intussusceptions are rare in Peutz–Jeghers syndrome. To the best of our knowledge, synchronous colocolic intussusception in association with Peutz–Jeghers syndrome has not been previously reported. Here we present a case of malignant jejunal mass and synchronous colocolic intussusceptions in a patient with Peutz–Jeghers syndrome. The British Institute of Radiology 2016-07-25 /pmc/articles/PMC6159284/ /pubmed/30363296 http://dx.doi.org/10.1259/bjrcr.20150314 Text en © 2017 The Authors. Published by the British Institute of Radiology http://creativecommons.org/licenses/by/4.0/ This is an open access article under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/) , which permits unrestricted use, distribution and reproduction in any medium, provided the original author and source are credited.
spellingShingle Case Report
Panta, Om Biju
Maharjan, Santosh
Manandhar, Sujan
Paudel, Sharma
Ghimire, Ram Kumar
A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome
title A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome
title_full A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome
title_fullStr A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome
title_full_unstemmed A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome
title_short A rare case of synchronous colocolic intussusception in association with Peutz–Jeghers syndrome
title_sort rare case of synchronous colocolic intussusception in association with peutz–jeghers syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6159284/
https://www.ncbi.nlm.nih.gov/pubmed/30363296
http://dx.doi.org/10.1259/bjrcr.20150314
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