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Multidisciplinary Perioperative Care for Children with Neuromuscular Disorders
Children with neuromuscular diseases present unique challenges to providing safe and appropriate perioperative care. Given the spectrum of disease etiologies and manifestations, this is a population that often requires specialized multidisciplinary care from pediatricians, geneticists, neurologists,...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6162674/ https://www.ncbi.nlm.nih.gov/pubmed/30213079 http://dx.doi.org/10.3390/children5090126 |
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author | Kynes, J. Matthew Blakely, Martin Furman, Kevin Burnette, William B. Modes, Katharina B. |
author_facet | Kynes, J. Matthew Blakely, Martin Furman, Kevin Burnette, William B. Modes, Katharina B. |
author_sort | Kynes, J. Matthew |
collection | PubMed |
description | Children with neuromuscular diseases present unique challenges to providing safe and appropriate perioperative care. Given the spectrum of disease etiologies and manifestations, this is a population that often requires specialized multidisciplinary care from pediatricians, geneticists, neurologists, dieticians, and pulmonologists which must also be coordinated with surgeons and anesthesiologists when these patients present for surgery. Several of these diseases also have specific pharmacologic implications for anesthesia, most notably mitochondrial disease and muscular dystrophies, which put them at additional risk during the perioperative period particularly in patients presenting without a formal diagnosis. Techniques and strategies to fully evaluate and optimize these patients preoperatively, manage them safely intraoperatively, and return them to their baseline status postoperative are particularly important in this vulnerable group of patients. Utilizing a review of inherited neuromuscular conditions, generalized perioperative concerns, and specific complications related to anesthesia, this article provides an overview of pertinent considerations and recommends a framework for management of these patients. |
format | Online Article Text |
id | pubmed-6162674 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | MDPI |
record_format | MEDLINE/PubMed |
spelling | pubmed-61626742018-10-16 Multidisciplinary Perioperative Care for Children with Neuromuscular Disorders Kynes, J. Matthew Blakely, Martin Furman, Kevin Burnette, William B. Modes, Katharina B. Children (Basel) Review Children with neuromuscular diseases present unique challenges to providing safe and appropriate perioperative care. Given the spectrum of disease etiologies and manifestations, this is a population that often requires specialized multidisciplinary care from pediatricians, geneticists, neurologists, dieticians, and pulmonologists which must also be coordinated with surgeons and anesthesiologists when these patients present for surgery. Several of these diseases also have specific pharmacologic implications for anesthesia, most notably mitochondrial disease and muscular dystrophies, which put them at additional risk during the perioperative period particularly in patients presenting without a formal diagnosis. Techniques and strategies to fully evaluate and optimize these patients preoperatively, manage them safely intraoperatively, and return them to their baseline status postoperative are particularly important in this vulnerable group of patients. Utilizing a review of inherited neuromuscular conditions, generalized perioperative concerns, and specific complications related to anesthesia, this article provides an overview of pertinent considerations and recommends a framework for management of these patients. MDPI 2018-09-12 /pmc/articles/PMC6162674/ /pubmed/30213079 http://dx.doi.org/10.3390/children5090126 Text en © 2018 by the authors. Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (http://creativecommons.org/licenses/by/4.0/). |
spellingShingle | Review Kynes, J. Matthew Blakely, Martin Furman, Kevin Burnette, William B. Modes, Katharina B. Multidisciplinary Perioperative Care for Children with Neuromuscular Disorders |
title | Multidisciplinary Perioperative Care for Children with Neuromuscular Disorders |
title_full | Multidisciplinary Perioperative Care for Children with Neuromuscular Disorders |
title_fullStr | Multidisciplinary Perioperative Care for Children with Neuromuscular Disorders |
title_full_unstemmed | Multidisciplinary Perioperative Care for Children with Neuromuscular Disorders |
title_short | Multidisciplinary Perioperative Care for Children with Neuromuscular Disorders |
title_sort | multidisciplinary perioperative care for children with neuromuscular disorders |
topic | Review |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6162674/ https://www.ncbi.nlm.nih.gov/pubmed/30213079 http://dx.doi.org/10.3390/children5090126 |
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