Good response to PAH-targeted drugs in a PVOD patient carrying Biallelic EIF2AK4 mutation

Pulmonary veno-occlusive disease (PVOD) is a rare and fatal cause of pulmonary arterial hypertension (PAH). Different from other types of PAH, PVOD patients have a dismal prognosis because of the progressive nature of pulmonary vascular involvement and fatal pulmonary edema induced by PAH-targeted d...

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Detalles Bibliográficos
Autores principales: Liang, Li, Su, Hua, Ma, Xiuqing, Zhang, Ruifeng
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2018
Materias:
Letter to the Editor
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6167821/
https://www.ncbi.nlm.nih.gov/pubmed/30285736
http://dx.doi.org/10.1186/s12931-018-0900-2

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6167821/
https://www.ncbi.nlm.nih.gov/pubmed/30285736
http://dx.doi.org/10.1186/s12931-018-0900-2

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