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Good response to PAH-targeted drugs in a PVOD patient carrying Biallelic EIF2AK4 mutation
Pulmonary veno-occlusive disease (PVOD) is a rare and fatal cause of pulmonary arterial hypertension (PAH). Different from other types of PAH, PVOD patients have a dismal prognosis because of the progressive nature of pulmonary vascular involvement and fatal pulmonary edema induced by PAH-targeted d...
| Autores principales: | , , , |
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| Formato: | Online Artículo Texto |
| Lenguaje: | English |
| Publicado: |
BioMed Central
2018
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| Materias: | |
| Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6167821/ https://www.ncbi.nlm.nih.gov/pubmed/30285736 http://dx.doi.org/10.1186/s12931-018-0900-2 |