Persistent Mullerian Duct Syndrome: A Single-Center Experience

CONTEXT: Persistent Mullerian duct syndrome (PMDS) is a rare disorder. It is a type of male pseudohermaphroditism, usually presenting as “Hernia Uteri Inguinalis”. AIMS: This study aims to present our experience of PMDS, over a 7-year period. SETTINGS AND DESIGN: Our center is a tertiary care facility, situated in Tamil Nadu, a southern state of India. SUBJECTS AND METHODS: This is a retrospective study. The study period was from 2007 to 2015. Seven cases presented during that period. The difficulties in diagnosis, treatment options discussed, along with a review of literature are presented. RESULTS: Seven cases of PMDS presented over 8 years. Only four were diagnosed preoperatively. Mullerian remnants were excised in five cases. CONCLUSIONS: PMDS is rare. Orchiopexy should be the goal of treatment.