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Mitochondrial Morphology, Function and Homeostasis Are Impaired by Expression of an N-terminal Calpain Cleavage Fragment of Ataxin-3

Alterations in mitochondrial morphology and function have been linked to neurodegenerative diseases, including Parkinson disease, Alzheimer disease and Huntington disease. Metabolic defects, resulting from dysfunctional mitochondria, have been reported in patients and respective animal models of all...

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Detalles Bibliográficos
Autores principales:	Harmuth, Tina, Prell-Schicker, Caroline, Weber, Jonasz J., Gellerich, Frank, Funke, Claudia, Drießen, Stefan, Magg, Janine C. D., Krebiehl, Guido, Wolburg, Hartwig, Hayer, Stefanie N., Hauser, Stefan, Krüger, Rejko, Schöls, Ludger, Riess, Olaf, Hübener-Schmid, Jeannette
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2018
Materias:	Neuroscience
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6192284/ https://www.ncbi.nlm.nih.gov/pubmed/30364204 http://dx.doi.org/10.3389/fnmol.2018.00368

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