Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature

Cutis laxa (CL) is a rare connective tissue disease characterized by a loose, wrinkled, and inelastic skin. Here, we report an unusual presentation in a 15-year-old male patient who is a known patient of CL who presented with bilateral pneumothorax. He was successfully managed initially by chest tub...

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Detalles Bibliográficos
Autores principales: Hajjar, Waseem M., Alrajeh, Areej S., Alturki, Lulwah S., Al-Nassar, Sami A., Hajjar, Adnan W.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2018
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6196669/
https://www.ncbi.nlm.nih.gov/pubmed/30416599
http://dx.doi.org/10.4103/atm.ATM_402_17
Descripción
Sumario:Cutis laxa (CL) is a rare connective tissue disease characterized by a loose, wrinkled, and inelastic skin. Here, we report an unusual presentation in a 15-year-old male patient who is a known patient of CL who presented with bilateral pneumothorax. He was successfully managed initially by chest tube insertion and then he was treated surgically with bilateral staged thoracoscopy, apical bullectomy, and pleurodesis with full uneventful recovery.

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