Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature

Cutis laxa (CL) is a rare connective tissue disease characterized by a loose, wrinkled, and inelastic skin. Here, we report an unusual presentation in a 15-year-old male patient who is a known patient of CL who presented with bilateral pneumothorax. He was successfully managed initially by chest tub...

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Autores principales: Hajjar, Waseem M., Alrajeh, Areej S., Alturki, Lulwah S., Al-Nassar, Sami A., Hajjar, Adnan W.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2018
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6196669/
https://www.ncbi.nlm.nih.gov/pubmed/30416599
http://dx.doi.org/10.4103/atm.ATM_402_17
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author Hajjar, Waseem M.
Alrajeh, Areej S.
Alturki, Lulwah S.
Al-Nassar, Sami A.
Hajjar, Adnan W.
author_facet Hajjar, Waseem M.
Alrajeh, Areej S.
Alturki, Lulwah S.
Al-Nassar, Sami A.
Hajjar, Adnan W.
author_sort Hajjar, Waseem M.
collection PubMed
description Cutis laxa (CL) is a rare connective tissue disease characterized by a loose, wrinkled, and inelastic skin. Here, we report an unusual presentation in a 15-year-old male patient who is a known patient of CL who presented with bilateral pneumothorax. He was successfully managed initially by chest tube insertion and then he was treated surgically with bilateral staged thoracoscopy, apical bullectomy, and pleurodesis with full uneventful recovery.
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spelling pubmed-61966692018-11-09 Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature Hajjar, Waseem M. Alrajeh, Areej S. Alturki, Lulwah S. Al-Nassar, Sami A. Hajjar, Adnan W. Ann Thorac Med Case Report Cutis laxa (CL) is a rare connective tissue disease characterized by a loose, wrinkled, and inelastic skin. Here, we report an unusual presentation in a 15-year-old male patient who is a known patient of CL who presented with bilateral pneumothorax. He was successfully managed initially by chest tube insertion and then he was treated surgically with bilateral staged thoracoscopy, apical bullectomy, and pleurodesis with full uneventful recovery. Medknow Publications & Media Pvt Ltd 2018 /pmc/articles/PMC6196669/ /pubmed/30416599 http://dx.doi.org/10.4103/atm.ATM_402_17 Text en Copyright: © 2018 Annals of Thoracic Medicine http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Hajjar, Waseem M.
Alrajeh, Areej S.
Alturki, Lulwah S.
Al-Nassar, Sami A.
Hajjar, Adnan W.
Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature
title Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature
title_full Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature
title_fullStr Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature
title_full_unstemmed Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature
title_short Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature
title_sort near-fatal presentation of bilateral pneumothorax in cutis laxa patient: case report, and review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6196669/
https://www.ncbi.nlm.nih.gov/pubmed/30416599
http://dx.doi.org/10.4103/atm.ATM_402_17
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