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Practicalities of a reduced volume formulation of a C1-INH concentrate for the treatment of hereditary angioedema: real-life experience

BACKGROUND: Hereditary angioedema (HAE) due to C1 esterase inhibitor (C1-INH) deficiency is characterized by recurrent swelling attacks that can be life-threatening if left untreated. Prompt treatment is vital during acute attacks; plasma-derived C1-INH (Berinert(®)) is one treatment currently licen...

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Detalles Bibliográficos
Autor principal:	Dempster, John
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2018
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6201499/ https://www.ncbi.nlm.nih.gov/pubmed/30386384 http://dx.doi.org/10.1186/s13223-018-0267-4

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