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Sjögren’s syndrome: state of the art on clinical practice guidelines

Sjögren’s syndrome (SS) is a complex autoimmune rheumatic disease that specifically targets salivary and lachrymal glands. As such, patients typically had ocular and oral dryness and salivary gland swelling. Moreover, skin, nasal and vaginal dryness are frequently present. In addition to dryness, mu...

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Autores principales: Romão, Vasco C, Talarico, Rosaria, Scirè, Carlo Alberto, Vieira, Ana, Alexander, Tobias, Baldini, Chiara, Gottenberg, Jacques-Eric, Gruner, Heidi, Hachulla, Eric, Mouthon, Luc, Orlandi, Martina, Pamfil, Cristina, Pineton de Chambrun, Marc, Taglietti, Marco, Toplak, Natasa, van Daele, Paul, van Laar, Jacob M, Bombardieri, Stefano, Schneider, Matthias, Smith, Vanessa, Cutolo, Maurizio, Mosca, Marta, Mariette, Xavier
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BMJ Publishing Group 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6203093/
https://www.ncbi.nlm.nih.gov/pubmed/30402274
http://dx.doi.org/10.1136/rmdopen-2018-000789
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author Romão, Vasco C
Talarico, Rosaria
Scirè, Carlo Alberto
Vieira, Ana
Alexander, Tobias
Baldini, Chiara
Gottenberg, Jacques-Eric
Gruner, Heidi
Hachulla, Eric
Mouthon, Luc
Orlandi, Martina
Pamfil, Cristina
Pineton de Chambrun, Marc
Taglietti, Marco
Toplak, Natasa
van Daele, Paul
van Laar, Jacob M
Bombardieri, Stefano
Schneider, Matthias
Smith, Vanessa
Cutolo, Maurizio
Mosca, Marta
Mariette, Xavier
author_facet Romão, Vasco C
Talarico, Rosaria
Scirè, Carlo Alberto
Vieira, Ana
Alexander, Tobias
Baldini, Chiara
Gottenberg, Jacques-Eric
Gruner, Heidi
Hachulla, Eric
Mouthon, Luc
Orlandi, Martina
Pamfil, Cristina
Pineton de Chambrun, Marc
Taglietti, Marco
Toplak, Natasa
van Daele, Paul
van Laar, Jacob M
Bombardieri, Stefano
Schneider, Matthias
Smith, Vanessa
Cutolo, Maurizio
Mosca, Marta
Mariette, Xavier
author_sort Romão, Vasco C
collection PubMed
description Sjögren’s syndrome (SS) is a complex autoimmune rheumatic disease that specifically targets salivary and lachrymal glands. As such, patients typically had ocular and oral dryness and salivary gland swelling. Moreover, skin, nasal and vaginal dryness are frequently present. In addition to dryness, musculoskeletal pain and fatigue are the hallmarks of this disease and constitute the classic symptom triad presented by the vast majority of patients. Up to 30% to 50 % of patients with SS may present systemic disease; moreover, there is an increased risk for the development of non-Hodgkin’s lymphoma that occurs in a minority of patients. The present work was developed in the framework of the European Reference Network (ERN) dedicated to Rare and Complex Connective Tissue and Musculoskeletal Diseases (ReCONNET). In line with its goals of aiming to improve early diagnosis, treatment and care of rare connective and musculoskeletal diseases, ERN-ReCONNET set to review the current state of clinical practice guidelines (CPGs) in the rare and complex connective tissue diseases of interest of the network. Therefore, the present work was aimed at providing a state of the art of CPGs for SS.
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spelling pubmed-62030932018-11-06 Sjögren’s syndrome: state of the art on clinical practice guidelines Romão, Vasco C Talarico, Rosaria Scirè, Carlo Alberto Vieira, Ana Alexander, Tobias Baldini, Chiara Gottenberg, Jacques-Eric Gruner, Heidi Hachulla, Eric Mouthon, Luc Orlandi, Martina Pamfil, Cristina Pineton de Chambrun, Marc Taglietti, Marco Toplak, Natasa van Daele, Paul van Laar, Jacob M Bombardieri, Stefano Schneider, Matthias Smith, Vanessa Cutolo, Maurizio Mosca, Marta Mariette, Xavier RMD Open Sjögren Syndrome Sjögren’s syndrome (SS) is a complex autoimmune rheumatic disease that specifically targets salivary and lachrymal glands. As such, patients typically had ocular and oral dryness and salivary gland swelling. Moreover, skin, nasal and vaginal dryness are frequently present. In addition to dryness, musculoskeletal pain and fatigue are the hallmarks of this disease and constitute the classic symptom triad presented by the vast majority of patients. Up to 30% to 50 % of patients with SS may present systemic disease; moreover, there is an increased risk for the development of non-Hodgkin’s lymphoma that occurs in a minority of patients. The present work was developed in the framework of the European Reference Network (ERN) dedicated to Rare and Complex Connective Tissue and Musculoskeletal Diseases (ReCONNET). In line with its goals of aiming to improve early diagnosis, treatment and care of rare connective and musculoskeletal diseases, ERN-ReCONNET set to review the current state of clinical practice guidelines (CPGs) in the rare and complex connective tissue diseases of interest of the network. Therefore, the present work was aimed at providing a state of the art of CPGs for SS. BMJ Publishing Group 2018-10-18 /pmc/articles/PMC6203093/ /pubmed/30402274 http://dx.doi.org/10.1136/rmdopen-2018-000789 Text en © Author(s) (or their employer(s)) 2018. Re-use permitted under CC BY-NC. No commercial re-use. See rights and permissions. Published by BMJ. This is an open access article distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited, appropriate credit is given, any changes made indicated, and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/.
spellingShingle Sjögren Syndrome
Romão, Vasco C
Talarico, Rosaria
Scirè, Carlo Alberto
Vieira, Ana
Alexander, Tobias
Baldini, Chiara
Gottenberg, Jacques-Eric
Gruner, Heidi
Hachulla, Eric
Mouthon, Luc
Orlandi, Martina
Pamfil, Cristina
Pineton de Chambrun, Marc
Taglietti, Marco
Toplak, Natasa
van Daele, Paul
van Laar, Jacob M
Bombardieri, Stefano
Schneider, Matthias
Smith, Vanessa
Cutolo, Maurizio
Mosca, Marta
Mariette, Xavier
Sjögren’s syndrome: state of the art on clinical practice guidelines
title Sjögren’s syndrome: state of the art on clinical practice guidelines
title_full Sjögren’s syndrome: state of the art on clinical practice guidelines
title_fullStr Sjögren’s syndrome: state of the art on clinical practice guidelines
title_full_unstemmed Sjögren’s syndrome: state of the art on clinical practice guidelines
title_short Sjögren’s syndrome: state of the art on clinical practice guidelines
title_sort sjögren’s syndrome: state of the art on clinical practice guidelines
topic Sjögren Syndrome
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6203093/
https://www.ncbi.nlm.nih.gov/pubmed/30402274
http://dx.doi.org/10.1136/rmdopen-2018-000789
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