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Isolated Intraventricular Rosai–Dorfman Disease
Rosai–Dorfman disease (RDD) is a benign histioproliferative disorder characterized by generalized lymphadenopathy, weakness, anemia, and rarely extranodal involvement. The disease affects the central nervous system (CNS) very rarely and at a relatively older age. Isolated intracranial involvement is...
Autores principales: | , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2018
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6208248/ https://www.ncbi.nlm.nih.gov/pubmed/30459919 http://dx.doi.org/10.4103/ajns.AJNS_134_18 |
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author | Patwardhan, Pranav Pramod Goel, Naina Atul |
author_facet | Patwardhan, Pranav Pramod Goel, Naina Atul |
author_sort | Patwardhan, Pranav Pramod |
collection | PubMed |
description | Rosai–Dorfman disease (RDD) is a benign histioproliferative disorder characterized by generalized lymphadenopathy, weakness, anemia, and rarely extranodal involvement. The disease affects the central nervous system (CNS) very rarely and at a relatively older age. Isolated intracranial involvement is very rare. RDD tends to present as dural masses mimicking meningioma, though very rare case reports describe isolated parenchymal involvement in the CNS. Only one case of intraventricular RDD has been described so far to the best of our knowledge. We present a very rare presentation of this disease as an isolated intraventricular presentation in the region of the atria of the lateral ventricles. |
format | Online Article Text |
id | pubmed-6208248 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-62082482018-11-20 Isolated Intraventricular Rosai–Dorfman Disease Patwardhan, Pranav Pramod Goel, Naina Atul Asian J Neurosurg Case Report Rosai–Dorfman disease (RDD) is a benign histioproliferative disorder characterized by generalized lymphadenopathy, weakness, anemia, and rarely extranodal involvement. The disease affects the central nervous system (CNS) very rarely and at a relatively older age. Isolated intracranial involvement is very rare. RDD tends to present as dural masses mimicking meningioma, though very rare case reports describe isolated parenchymal involvement in the CNS. Only one case of intraventricular RDD has been described so far to the best of our knowledge. We present a very rare presentation of this disease as an isolated intraventricular presentation in the region of the atria of the lateral ventricles. Medknow Publications & Media Pvt Ltd 2018 /pmc/articles/PMC6208248/ /pubmed/30459919 http://dx.doi.org/10.4103/ajns.AJNS_134_18 Text en Copyright: © 2018 Asian Journal of Neurosurgery http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Patwardhan, Pranav Pramod Goel, Naina Atul Isolated Intraventricular Rosai–Dorfman Disease |
title | Isolated Intraventricular Rosai–Dorfman Disease |
title_full | Isolated Intraventricular Rosai–Dorfman Disease |
title_fullStr | Isolated Intraventricular Rosai–Dorfman Disease |
title_full_unstemmed | Isolated Intraventricular Rosai–Dorfman Disease |
title_short | Isolated Intraventricular Rosai–Dorfman Disease |
title_sort | isolated intraventricular rosai–dorfman disease |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6208248/ https://www.ncbi.nlm.nih.gov/pubmed/30459919 http://dx.doi.org/10.4103/ajns.AJNS_134_18 |
work_keys_str_mv | AT patwardhanpranavpramod isolatedintraventricularrosaidorfmandisease AT goelnainaatul isolatedintraventricularrosaidorfmandisease |