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Case report of surgical treatment of scoliosis caused by neurofibroma located posterior mediastinum

BACKGROUND: Neurofibromatosis type 1 (NF-1) is often associated with various orthopedic disorders, especially scoliosis. Spinal deformity in patients with NF-1 can be induced by localized neurofibromas. CASE PRESENTATION: Scoliosis can be induced by a localized neurofibroma. A 12-year-old boy diagno...

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Autores principales: Motono, Nozomu, Kawaguchi, Masahito, Kawahara, Norio, Uramoto, Hidetaka
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6222067/
https://www.ncbi.nlm.nih.gov/pubmed/30408738
http://dx.doi.org/10.1016/j.ijscr.2018.10.071
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author Motono, Nozomu
Kawaguchi, Masahito
Kawahara, Norio
Uramoto, Hidetaka
author_facet Motono, Nozomu
Kawaguchi, Masahito
Kawahara, Norio
Uramoto, Hidetaka
author_sort Motono, Nozomu
collection PubMed
description BACKGROUND: Neurofibromatosis type 1 (NF-1) is often associated with various orthopedic disorders, especially scoliosis. Spinal deformity in patients with NF-1 can be induced by localized neurofibromas. CASE PRESENTATION: Scoliosis can be induced by a localized neurofibroma. A 12-year-old boy diagnosed with neurofibromatosis type 1 had severe scoliosis caused by a neurofibroma located in the posterior mediastinum. We performed two-stage procedure involving the extirpation of the neurofibroma in the lateral position, and posterior spinal fusion with segmental spinal instrumentation for the scoliosis in the prone position. DISCUSSION: The optimum surgical approach for the extirpation of neurofibroma located in the posterior mediastinal remains to be established. It may be difficult to extirpate a tumor in this position via a posterior approach alone, as the tumor is surrounded by several tissue, e.g. azygos vein, trachea and esophagus. In our case, we first extirpated the tumor located in the posterior mediastinum via a posterolateral incision in the right lateral position. With this approach, it may be easy to confirm the safe relationship between the tumor and surrounding tissue. CONCLUSIONS: We safely performed a two-stage procedure involving the extirpation of a neurofibroma in the lateral position, and posterior spinal fusion with segmental spinal instrumentation for scoliosis in the prone position.
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spelling pubmed-62220672018-11-29 Case report of surgical treatment of scoliosis caused by neurofibroma located posterior mediastinum Motono, Nozomu Kawaguchi, Masahito Kawahara, Norio Uramoto, Hidetaka Int J Surg Case Rep Article BACKGROUND: Neurofibromatosis type 1 (NF-1) is often associated with various orthopedic disorders, especially scoliosis. Spinal deformity in patients with NF-1 can be induced by localized neurofibromas. CASE PRESENTATION: Scoliosis can be induced by a localized neurofibroma. A 12-year-old boy diagnosed with neurofibromatosis type 1 had severe scoliosis caused by a neurofibroma located in the posterior mediastinum. We performed two-stage procedure involving the extirpation of the neurofibroma in the lateral position, and posterior spinal fusion with segmental spinal instrumentation for the scoliosis in the prone position. DISCUSSION: The optimum surgical approach for the extirpation of neurofibroma located in the posterior mediastinal remains to be established. It may be difficult to extirpate a tumor in this position via a posterior approach alone, as the tumor is surrounded by several tissue, e.g. azygos vein, trachea and esophagus. In our case, we first extirpated the tumor located in the posterior mediastinum via a posterolateral incision in the right lateral position. With this approach, it may be easy to confirm the safe relationship between the tumor and surrounding tissue. CONCLUSIONS: We safely performed a two-stage procedure involving the extirpation of a neurofibroma in the lateral position, and posterior spinal fusion with segmental spinal instrumentation for scoliosis in the prone position. Elsevier 2018-11-01 /pmc/articles/PMC6222067/ /pubmed/30408738 http://dx.doi.org/10.1016/j.ijscr.2018.10.071 Text en © 2018 The Authors http://creativecommons.org/licenses/by/4.0/ This is an open access article under the CC BY license (http://creativecommons.org/licenses/by/4.0/).
spellingShingle Article
Motono, Nozomu
Kawaguchi, Masahito
Kawahara, Norio
Uramoto, Hidetaka
Case report of surgical treatment of scoliosis caused by neurofibroma located posterior mediastinum
title Case report of surgical treatment of scoliosis caused by neurofibroma located posterior mediastinum
title_full Case report of surgical treatment of scoliosis caused by neurofibroma located posterior mediastinum
title_fullStr Case report of surgical treatment of scoliosis caused by neurofibroma located posterior mediastinum
title_full_unstemmed Case report of surgical treatment of scoliosis caused by neurofibroma located posterior mediastinum
title_short Case report of surgical treatment of scoliosis caused by neurofibroma located posterior mediastinum
title_sort case report of surgical treatment of scoliosis caused by neurofibroma located posterior mediastinum
topic Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6222067/
https://www.ncbi.nlm.nih.gov/pubmed/30408738
http://dx.doi.org/10.1016/j.ijscr.2018.10.071
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