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Imaging and clinical findings in a case of linear scleroderma en coup de sabre

We present the case of a 58-year-old female presenting with acute onset headache and decrease in left-sided facial sensation. The patient's background included diabetes Type 2, hypertension, migraine, anxiety with depression and scleroderma in her childhood. Imaging revealed foci of right front...

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Autores principales: Corbally, Conal M, Breckenridge, Andrew, Jampana, Ravi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The British Institute of Radiology 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6243297/
https://www.ncbi.nlm.nih.gov/pubmed/30460009
http://dx.doi.org/10.1259/bjrcr.20150203
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author Corbally, Conal M
Breckenridge, Andrew
Jampana, Ravi
author_facet Corbally, Conal M
Breckenridge, Andrew
Jampana, Ravi
author_sort Corbally, Conal M
collection PubMed
description We present the case of a 58-year-old female presenting with acute onset headache and decrease in left-sided facial sensation. The patient's background included diabetes Type 2, hypertension, migraine, anxiety with depression and scleroderma in her childhood. Imaging revealed foci of right frontal calcification and confluent white matter changes, reported as sequelae of a previous ischaemic episode. Following a second presentation with the same symptoms, further imaging showed a linear soft tissue scar overlying these changes, which suggested a diagnosis of linear scleroderma (en coup de sabre). On questioning, it was found that this had developed during the patient's late teens but had not progressed since that time. Coup de sabre type linear scleroderma is often associated with intracranial imaging findings, even in the absence of symptoms. The pathogenesis of neurological symptoms is poorly understood but does seem to respond to immunosuppression.
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spelling pubmed-62432972018-11-20 Imaging and clinical findings in a case of linear scleroderma en coup de sabre Corbally, Conal M Breckenridge, Andrew Jampana, Ravi BJR Case Rep Case Report We present the case of a 58-year-old female presenting with acute onset headache and decrease in left-sided facial sensation. The patient's background included diabetes Type 2, hypertension, migraine, anxiety with depression and scleroderma in her childhood. Imaging revealed foci of right frontal calcification and confluent white matter changes, reported as sequelae of a previous ischaemic episode. Following a second presentation with the same symptoms, further imaging showed a linear soft tissue scar overlying these changes, which suggested a diagnosis of linear scleroderma (en coup de sabre). On questioning, it was found that this had developed during the patient's late teens but had not progressed since that time. Coup de sabre type linear scleroderma is often associated with intracranial imaging findings, even in the absence of symptoms. The pathogenesis of neurological symptoms is poorly understood but does seem to respond to immunosuppression. The British Institute of Radiology 2016-11-02 /pmc/articles/PMC6243297/ /pubmed/30460009 http://dx.doi.org/10.1259/bjrcr.20150203 Text en © 2016 The Authors. Published by the British Institute of Radiology http://creativecommons.org/licenses/by/4.0/ This is an open access article under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/) , which permits unrestricted use, distribution and reproduction in any medium, provided the original author and source are credited.
spellingShingle Case Report
Corbally, Conal M
Breckenridge, Andrew
Jampana, Ravi
Imaging and clinical findings in a case of linear scleroderma en coup de sabre
title Imaging and clinical findings in a case of linear scleroderma en coup de sabre
title_full Imaging and clinical findings in a case of linear scleroderma en coup de sabre
title_fullStr Imaging and clinical findings in a case of linear scleroderma en coup de sabre
title_full_unstemmed Imaging and clinical findings in a case of linear scleroderma en coup de sabre
title_short Imaging and clinical findings in a case of linear scleroderma en coup de sabre
title_sort imaging and clinical findings in a case of linear scleroderma en coup de sabre
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6243297/
https://www.ncbi.nlm.nih.gov/pubmed/30460009
http://dx.doi.org/10.1259/bjrcr.20150203
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