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Label-Free Quantitative Proteomics in a Methylmalonyl-CoA Mutase-Silenced Neuroblastoma Cell Line
Methylmalonic acidemias (MMAs) are inborn errors of metabolism due to the deficient activity of methylmalonyl-CoA mutase (MUT). MUT catalyzes the formation of succinyl-CoA from methylmalonyl-CoA, produced from propionyl-CoA catabolism and derived from odd chain fatty acids β-oxidation, cholesterol,...
Autores principales: | Costanzo, Michele, Cevenini, Armando, Marchese, Emanuela, Imperlini, Esther, Raia, Maddalena, Del Vecchio, Luigi, Caterino, Marianna, Ruoppolo, Margherita |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6275031/ https://www.ncbi.nlm.nih.gov/pubmed/30428564 http://dx.doi.org/10.3390/ijms19113580 |
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