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Pulmonary arterial dilation with normal pulmonary artery pressure in sarcoidosis
In this paper we present a clinical case that has improved on our knowledge and our curiosity about sarcoidosis. We report a case of a patient known to have pulmonary sarcoidosis, who presents with respiratory failure with severe hypercapnia. Following thorough investigations this patient was recogn...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6293960/ https://www.ncbi.nlm.nih.gov/pubmed/30613564 http://dx.doi.org/10.4103/jfmpc.jfmpc_263_18 |
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author | Al-khateeb, Anas Meng, William Kadri, Muqueet Bellary, Sharath Sharma, Hari Miller, Richard |
author_facet | Al-khateeb, Anas Meng, William Kadri, Muqueet Bellary, Sharath Sharma, Hari Miller, Richard |
author_sort | Al-khateeb, Anas |
collection | PubMed |
description | In this paper we present a clinical case that has improved on our knowledge and our curiosity about sarcoidosis. We report a case of a patient known to have pulmonary sarcoidosis, who presents with respiratory failure with severe hypercapnia. Following thorough investigations this patient was recognized to have three unique yet interrelated aspects of clinical manifestations. He was found to have severe bilateral diaphragmatic hypokinesis, dilated pulmonary vasculature with normal pulmonary pressure, and a state of high output right sided heart failure. We propose an explanation of such a presentation, while we attempted to discuss possible alternative mechanisms. In conclusion, we report this case as the first recognized case of sarcoidosis to be related to diffusely dilated pulmonary vasculature of normal vascular pressure. |
format | Online Article Text |
id | pubmed-6293960 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2018 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-62939602019-01-04 Pulmonary arterial dilation with normal pulmonary artery pressure in sarcoidosis Al-khateeb, Anas Meng, William Kadri, Muqueet Bellary, Sharath Sharma, Hari Miller, Richard J Family Med Prim Care Case Report In this paper we present a clinical case that has improved on our knowledge and our curiosity about sarcoidosis. We report a case of a patient known to have pulmonary sarcoidosis, who presents with respiratory failure with severe hypercapnia. Following thorough investigations this patient was recognized to have three unique yet interrelated aspects of clinical manifestations. He was found to have severe bilateral diaphragmatic hypokinesis, dilated pulmonary vasculature with normal pulmonary pressure, and a state of high output right sided heart failure. We propose an explanation of such a presentation, while we attempted to discuss possible alternative mechanisms. In conclusion, we report this case as the first recognized case of sarcoidosis to be related to diffusely dilated pulmonary vasculature of normal vascular pressure. Medknow Publications & Media Pvt Ltd 2018 /pmc/articles/PMC6293960/ /pubmed/30613564 http://dx.doi.org/10.4103/jfmpc.jfmpc_263_18 Text en Copyright: © 2018 Journal of Family Medicine and Primary Care http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Al-khateeb, Anas Meng, William Kadri, Muqueet Bellary, Sharath Sharma, Hari Miller, Richard Pulmonary arterial dilation with normal pulmonary artery pressure in sarcoidosis |
title | Pulmonary arterial dilation with normal pulmonary artery pressure in sarcoidosis |
title_full | Pulmonary arterial dilation with normal pulmonary artery pressure in sarcoidosis |
title_fullStr | Pulmonary arterial dilation with normal pulmonary artery pressure in sarcoidosis |
title_full_unstemmed | Pulmonary arterial dilation with normal pulmonary artery pressure in sarcoidosis |
title_short | Pulmonary arterial dilation with normal pulmonary artery pressure in sarcoidosis |
title_sort | pulmonary arterial dilation with normal pulmonary artery pressure in sarcoidosis |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6293960/ https://www.ncbi.nlm.nih.gov/pubmed/30613564 http://dx.doi.org/10.4103/jfmpc.jfmpc_263_18 |
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